Neuropathology and Applied Neurobiology

Article	Citations
Role of Astrocytic and Microglial Phenotype in the Biology of Hippocampal Sclerosis	143
Oral Abstracts	65
Neuronal infection is a major pathogenetic mechanism and cause of fatalities in human acute Nipah virus encephalitis	58
Neuropathological Characterisation of McLeod Syndrome With a Proposed New Grading System	36
Novel naturally occurring autoantibodies attenuate α‐synuclein pathology in a mouse model of Parkinson's disease	34
Editorial	29
Intelligence quotient–genotype association in dystrophinopathies: A systematic review and meta‐analysis	28
Paediatric astroblastoma‐like neuroepithelial tumour of the spinal cord with a MAMLD1‐BEND2 rearrangement	27
An autopsy case of late‐onset spinocerebellar atrophy type 14	27
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Author Index	22
Erratum	22
Myopathology and Immune Profile of Granulomatous Myositis in Sarcoid Myopathy	21
Rapid bacterial identification from formalin‐fixed paraffin‐embedded neuropathology specimens using 16S rDNA nanopore sequencing	20
Myostatin in idiopathic inflammatory myopathies: Serum assessment and disease activity	19
A novel SREBF1::NACC1 gene fusion in an unclassifiable intracranial tumour	19
Synaptic gene expression changes in frontotemporal dementia due to the MAPT 10 + 16 mutation	18
Anaplastic ganglioglioma—A diagnosis comprising several distinct tumour types	18
Analysing cerebrospinal fluid with explainable deep learning: From diagnostics to insights	17
Neuronal and astrocytic tetraploidy is increased in drug‐resistant epilepsy	17
Response letter: Complexities in pericyte markers	17
The S1PR2‐CCL2‐BDNF‐TrkB pathway mediates neuroinflammation and motor incoordination in hyperammonaemia	17
Issue Information	16
Cover Image, Volume 50, Issue 3	16

Genetic inhibition of PDK1 robustly reduces plaque deposition and ameliorates gliosis in the 5×FAD mouse model of Alzheimer's disease	16
124th Meeting of the British Neuropathological Society The View, Royal College of Surgeons of England, Lincoln's Inn Fields, London	16
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Perineuronal nets are phagocytosed by MMP‐9 expressing microglia and astrocytes in the SOD1 G93A ALS mouse model	15
A standardised protocol for blood and cerebrospinal fluid collection and processing for biomarker research in ataxia	15
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Phenotypic and epigenetic heterogeneity in FGFR2 ‐fused glial and glioneuronal tumours	14
Adult‐onset Alexander disease with unusual inflammatory features and a novel GFAP mutation in two patients	14
Application of Oral Mucosal Epithelial Cells in Noninvasive Pathological Diagnosis of Neuronal Intranuclear Inclusion Disease	14
Evidence of neural crest cell origin of a DICER1 mutant CNS sarcoma in a child with DICER1 syndrome and NRAS‐mutant neurocutaneous melanosis	14
Fibrodysplasia ossificans progressiva: Histopathological implications of aberrant bone morphogenic protein signalling for CNS dysgenesis	14
m6A mRNA methylation in human brain is disrupted in Lewy body disorders	13
Robust methylation‐based classification of brain tumours using nanopore sequencing	13
Microglia induce an interferon‐stimulated gene expression profile in glioblastoma and increase glioblastoma resistance to temozolomide	13
Epigenetic age acceleration is associated with oligodendrocyte proportions in MSA and control brain tissue	13
RNA sequencing of peripheral blood in amyotrophic lateral sclerosis reveals distinct molecular subtypes: Considerations for biomarker discovery	13
TDP‐43 pathology and functional deficits in wild‐type and ALS/FTD mutant cyclin F mouse models	13
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WNT‐activated, MYC ‐amplified medulloblastoma displaying intratumoural heterogeneity	12
126th Meeting of the British Neuropathological Society The View, Royal College of Surgeons of England, Lincoln's Inn Fields, London	12
Comprehensive analysis of intratumoural heterogeneity of somatic copy number alterations in diffuse glioma reveals clonality‐dependent prognostic patterns	12
Hippocampal dentate granule cells in temporal lobe epilepsy: A morphometry and transcriptomic study	12
Is islet amyloid polypeptide indeed expressed in the human brain?	12
The blood–CSF–brain route of neurological disease: The indirect pathway into the brain	12
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The genomic landscape of dysembryoplastic neuroepithelial tumours and a comprehensive analysis of recurrent cases	11
Issue Information	11
Intramuscular Nerve Bundles Reflect TDP‐43 Pathology in the Medulla and Spinal Cord of ALS Patients	10
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Interferon‐gamma contributes to disease progression in the Ndufs4 (−/−) model of Leigh syndrome	10
Axonal response of mitochondria to demyelination and complex IV activity within demyelinated axons in experimental models of multiple sclerosis	10
Fibroblast growth factor 9 (FGF9)‐mediated neurodegeneration: Implications for progressive multiple sclerosis?	10
Nanopore sequencing identifies Borrelia miyamotoi as an unexpected cause of meningitis after B cell depletion	10
Pathological Characterisation of Posterior Cortical Atrophy in Comparison With Amnestic Alzheimer's Disease	9
Issue Information	9
Quantitative cellular changes in multiple system atrophy brains	9
Muscle biopsy practices in the evaluation of neuromuscular disease: A systematic literature review	9
Issue Information	9
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Corrigendum	9
Atypical teratoid/rhabdoid tumour‐TYR subtype arising in the setting of germline ring chromosome 22: An uncommon form of tumour predisposition	8
HnRNP K mislocalisation in neurons of the dentate nucleus is a novel neuropathological feature of neurodegenerative disease and ageing	8
Proteomic profiling of polyglucosan bodies associated with glycogenin‐1 deficiency in skeletal muscle	8
Low‐grade diffusely infiltrative tumour (LGDIT), SMARCB1‐mutant: A clinical and histopathological distinct entity showing epigenetic similarity with ATRT‐MYC	8
Adult brain tumour research in 2024: Status, challenges and recommendations	8
Amino‐terminally elongated Aβ peptides are generated by the secreted metalloprotease ADAMTS4 and deposit in a subset of Alzheimer's disease brains	8
Corrigendum	8
Cytoplasmic HDAC4 recovers synaptic function in the 3×Tg mouse model of Alzheimer's disease	8
Unfolded protein response markers Grp78 and eIF2alpha are upregulated with increasing alpha‐synuclein levels in Lewy body disease	7
Diagnostic accuracy of 1p/19q codeletion tests in oligodendroglioma: A comprehensive meta‐analysis based on a Cochrane systematic review	7

GFAP expression in the brain during human postnatal development	7
Regional redistribution of CB1 cannabinoid receptors in human foetal brains with Down's syndrome and their functional modifications in Ts65Dn +/+ mic	7
Letter to the editor	7
Ageing‐related tau astrogliopathy severely affecting the substantia nigra	7
Soluble amyloid‐β dimers are resistant to amyloid‐β prion conversion in vivo suggesting antiprion properties	6
Cerebellar phenotypes in germline PTEN mutation carriers	6
Issue Information	6
LMNB1 ‐duplication mediated nuclear architecture alteration and demyelination of cerebral white matter in a patient with ADLD	6
The SPTLC1 p.S331 mutation bridges sensory neuropathy and motor neuron disease and has implications for treatment	6
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Multiplex Immunofluorescent Analysis of Alpha‐Synuclein in Nigral Lewy Bodies With Heat‐Induced Antibody Stripping Reveals an Intricate Multilayered Structure	6
Regulation of CNS pathology by Serpina3n/SERPINA3: The knowns and the puzzles	6
Issue Information	6
Identification of a novel heterozygous DYSF variant in a large family with a dominantly‐inherited dysferlinopathy	5
Mechanisms of COVID‐19‐associated olfactory dysfunction	5
Methyl donor supplementation reduces phospho‐Tau, Fyn and demethylated protein phosphatase 2A levels and mitigates learning and motor deficits in a mouse model of tauopathy	5
Issue Information	5
Dysfunction of the blood–brain barrier in Alzheimer's disease: Evidence from human studies	5
Cover Image, Volume 50, Issue 1	5
Metastatic Bifocal Germinoma With Dramatic Early Steroid Response, Utility of Circulating miR‐371a‐3p and Vinblastine Monotherapy Prior to Definitive Craniospinal Irradiation	5
Relationships Between Alcohol Intake and Mitochondrial DNA Methylation in the Human Prefrontal Cortex and Nucleus Accumbens	5
125th Meeting of the British Neuropathological Society The View, Royal College of Surgeons of England, Lincoln's Inn Fields, London	5
A novel homozygous nonsense variant in COL12A1 causes myopathic Ehlers‐Danlos syndrome: A case report and literature review	5
TAF15 and Transportin 1 in Intranuclear Inclusions of Neuronal Intranuclear Inclusion Disease	5
Ectopic expression of neuronal adenosine kinase, a biomarker in mesial temporal lobe epilepsy without hippocampal sclerosis	5
Computational Analysis of SOD1‐G93A Mouse Muscle Biomarkers for Comprehensive Assessment of ALS Progression	4
Cortical morphometric vulnerability to generalised epilepsy reflects chromosome‐ and cell type‐specific transcriptomic signatures	4
Pathological substrate of memory impairment in multiple system atrophy	4
An Intracerebrally‐Infected Mouse Model of Enterovirus A71 Demonstrates Restricted Inter‐Neuronal Spread Within the Brain Parenchyma Despite Strong SCARB2 Expression	4
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Correction to “Neuropathological Characterisation of McLeod Syndrome With a Proposed New Grading System”	4
Loss of IDH mutation or secondary tumour manifestation? Evolution of an IDH‐mutant and 1p/19q‐codeleted oligodendroglioma after 15 years of continuous temozolomide treatment and radiotherapy: A case r	4
Phosphorylation of MAP 1A regulates hyperphosphorylation of Tau in Alzheimer's disease model	4
PLAG‐Family Amplified CNS Embryonal Tumour With PLAG1 Immunohistochemical Expression: Expanding the Spectrum of Diagnostic Tools	4
Issue Information	4
Analysis of a pituitary tumour with histological features of central neurocytoma points towards the emergence of a new entity recognisable by a specific epigenetic signature	4
Neuroinvasion via Peripheral Nerves in Epidemic Viral Encephalitis Caused by Enterovirus, Orthoflavivirus and SARS‐Coronavirus	4
Issue Information	4
Distinguishing post‐translational modifications in dominantly inherited frontotemporal dementias: FTLD‐TDP Type A ( GRN ) vs Type B (	4
Muscleblind‐like 2 knockout shifts adducin 1 isoform expression and alters dendritic spine dynamics of cortical neurons during brain development	4
Simultaneous Nbs1 and p53 inactivation in neural progenitors triggers high‐grade gliomas	4
Standardised TruAI Automated Quantification of Intracellular Neuromelanin Granules in Human Brain Tissue Sections	4
Refining Muscle Morphometry Through Machine Learning and Spatial Analysis	4
Psychotic symptoms in frontotemporal dementia with TDP‐43 tend to be associated with type B pathology	4
Classification of diseases with accumulation of Tau protein	4
Skeletal muscle involvement in systemic amyloidosis is often overlooked	4
The molecular mechanisms that underlie IGHMBP2 ‐related diseases	4
Central Nervous System Kinase‐Altered Spindle Cell Neoplasm: A Case Series of an Emerging Tumour Type	4
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Artificial intelligence in histopathological image analysis of central nervous system tumours: A systematic review	4
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Respiratory chain dysfunction in perifascicular muscle fibres in patients with dermatomyositis is associated with mitochondrial DNA depletion	3
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Paths to hippocampal damage in neuromyelitis optica spectrum disorders	3
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Cover Image, Volume 48, Issue 5	3
Unveiling the identities of null cell tumours: Epigenomics corroborate subtle histological cues in pituitary neuroendocrine tumour/adenoma classification	3
Early loss of locus coeruleus innervation promotes cognitive and neuropathological changes before amyloid plaque deposition in a transgenic rat model of Alzheimer's disease	3
Testing Meningiomas With Methylation Arrays: Insights and Recommendations From a Large Single‐Centre Study	3
A reassessment of spinal cord pathology in severe infantile spinal muscular atrophy	3
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Oxygen treatment reduces neurological deficits and demyelination in two animal models of multiple sclerosis	3
Change in the molecular properties of CH1641 prions after transmission to wild‐type mice: Evidence for a single strain	3
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Issue Information	3
Slow disease progression and characteristic TDP‐43 inclusions in a patient with familial amyotrophic lateral sclerosis carrying a TARDBP G357S variant	2
Identical Seeding Characteristics and Cryo‐EM Filament Structures in FTLD‐Synuclein and Typical Multiple System Atrophy	2
Recurrent posterior fossa group A (PFA) ependymoma in a young child with constitutional mismatch repair deficiency (CMMRD)	2
A Variant of OTUD3 in Early‐Onset Parkinsonism	2
Protein Coaggregation in Caribbean Atypical Parkinsonism: The Contribution of Annonacin	2
Nanoscale reorganisation of synaptic proteins in Alzheimer's disease	2
Genotype–Phenotype Correlation in Progressive External Ophthalmoplegia: Insights From a Retrospective Analysis	2
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Clinicopathological Characteristics and Immune Microenvironment of Posterior Pituitary Tumours	2
A high‐throughput single‐cell RNA expression profiling method identifies human pericyte markers	2
Investigating key factors underlying neurodegeneration linked to alpha‐synuclein spread	2
Elevated expression of urokinase plasminogen activator in rodent models and patients with cerebral amyloid angiopathy	2
Diffuse infiltrating tumour with the molecular profile of an atypical teratoid rhabdoid tumour (AT/RT SHH‐1B) in an adult patient	2
Post‐mortem 7T MR imaging and neuropathology in middle stage juvenile‐onset Huntington disease: A case report	2
TAPPing into the potential of inducible tau/APP transgenic mice	2

Tuberous sclerosis complex‐1 (TSC1) contributes to selective neuronal vulnerability in Alzheimer's disease	2
Progressive hemispheric atrophy in HIV: A Rasmussen's‐like variant of CD8 encephalitis?	2
Pathogenic variants of Valosin‐containing protein induce lysosomal damage and transcriptional activation of autophagy regulators in neuronal cells	2
The contribution of brain banks to knowledge discovery in amyotrophic lateral sclerosis: A systematic review	2
Chronic traumatic encephalopathy neuropathologic change in former Australian rugby players	2
Cu II (atsm) significantly decreases microglial reactivity in patients with sporadic amyotrophic lateral sclerosis	2