Annals of Neurology

Papers
(The median citation count of Annals of Neurology is 3. The table below lists those papers that are above that threshold based on CrossRef citation counts [max. 250 papers]. The publications cover those that have been published in the past four years, i.e., from 2021-07-01 to 2025-07-01.)
ArticleCitations
Annals of Neurology: Volume 90, Number S27, October 2021181
Issue Information140
Network Localization of Awareness in Visual and Motor Anosognosia131
Elevated Cerebrospinal Fluid Ubiquitin Carboxyl‐Terminal Hydrolase Isozyme L1 in Asymptomatic C9orf72 Hexanucleotide Repeat Expansion Carriers128
Efficacy and Safety of Ofatumumab Treatment for Anti‐NMDA Receptor Autoimmune Encephalitis (OFFAE): A Prospective, Multicenter Cohort Study127
Association of Retromer Deficiency and Tau Pathology in Down Syndrome110
Issue Information100
Annals of Neurology: Volume 97, Number 1, January 202596
Carotid Stent Fracture95
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A Role for Insulin‐like Growth Factor 1 in the Generation of Epileptic Spasms in a murine model93
MS‐Driven Metabolic Alterations Are Recapitulated in iPSC‐Derived Astrocytes89
Effect of Imaging Markers on Reperfusion Therapy in Basilar Artery Occlusion88
Cortical Microhemorrhage Presentation of Small Vessel Primary Angiitis of the Central Nervous System81
Vertebral Artery Pseudoaneurysm: Novel Marker of Bow Hunter's Syndrome80
Supratentorial Lymphocytic Inflammation with Parenchymal Perivascular Enhancement Responsive to Steroids: A Potentially Overlooked Diagnosis80
Prevalence of Cerebral Amyloid Angiopathy and Associated Risk of Subsequent Ischemic and Hemorrhagic Stroke and Mortality in a Nationwide Cohort78
Hypoparathyroidism Associated with Vascular Centrum Semiovale Calcifications77
Furthering Female Faculty: An American Neurological Association/Association of University Professors of Neurology Perspective75
HLA Associations of Intrathecal IgG Production against Specific Viruses in Multiple Sclerosis71
Interactions between High Seroreactivity to Human Herpes Virus 6A and Epstein–Barr Virus in MS Development: A Presymptomatic Case–Control Study70
A Letter Concerning a Role for Blood–Brain Barrier Dysfunction in Delirium following Noncardiac Surgery in Older Adults69
The Use of Antihypertensive Medication and In Vivo Alzheimer's Disease Pathology67
A Managed Care System with Telemedicine Support for Neurological Emergencies67
Cerebrospinal Fluid Flow in Patients with Huntington's Disease67
Management of Cerebral Venous Thrombosis Due to Adenoviral COVID‐19 Vaccination66
Staufen Impairs Autophagy in Neurodegeneration66
Guanylate Kinase 1 Deficiency: A Novel and Potentially Treatable Mitochondrial DNA Depletion/Deletions Disease64
Epidemiology, Survival, and Clinical Characteristics of Inclusion Body Myositis64
Before, during, and after: An Argument for Safety and Improved Outcome of Thrombolysis in Acute Ischemic Stroke with Direct Oral Anticoagulant Treatment57
Dysregulation of Gut Microbiota‐Derived Neuromodulatory Amino Acid Metabolism in Human Immunodeficiency Virus‐Associated Neurocognitive Disorder: An Integrative Metagenomic and Metabolomic 56
Septin‐5 and ‐7‐IgGs: Neurologic, Serologic, and Pathophysiologic Characteristics56
Human Brain Resilience: A Call to Action54
Suvorexant Acutely Decreases Tau Phosphorylation and Aβ in the Human CNS54
Blood Pressure after Successful Endovascular Therapy: A Systematic Review and Meta‐Analysis of Randomized Control Trials54
Severity of GNAO1‐Related Disorder Correlates with Changes in G‐Protein Function53
Diet, Pace of Biological Aging, and Risk of Dementia in the Framingham Heart Study52
Plasma Metabolites Link Dietary Patterns to Stroke Risk51
Probabilistic Mapping Reveals Optimal Stimulation Site in Essential Tremor48
Biological Age Acceleration and Motoric Cognitive Risk Syndrome48
Cover Image47
Annals of Neurology: Volume 90, Number S26, September 202147
Annals of Neurology: Volume 94, Number S30, September 202347
Micro‐Doses of DNP Preserve Motor and Muscle Function with a Period of Functional Recovery in Amyotrophic Lateral Sclerosis Mice46
Issue Information46
RAN Translation of C9orf72‐Related Dipeptide Repeat Proteins in Zebrafish Recapitulates Hallmarks of Amyotrophic Lateral Sclerosis and Identifies Hypothermia as a Therapeutic Strategy45
Sports Concussion and Category Mistakes45
Longitudinal Imaging Biomarkers Correlate with Progressive Motor Deficit in the Mouse Model of Charlevoix‐Saguenay Ataxia45
MEK Pathway Inhibitor‐Mediated Response in BRAF V600‐Mutant Melanoma with Brain Parenchymal and Leptomeningeal Metastases45
Tenascin‐R Autoimmunity: Isolated Tremor Reversed with Immunotherapy45
Reply to “Core Penumbral Mismatch: An Independent Predictor of Stroke Poorer Outcome”45
Illusions of Self‐Motion during Magnetic Resonance‐Guided Focused Ultrasound Thalamotomy for Tremor45
APOE2 Exacerbates TDP‐43 Related Toxicity in the Absence of Alzheimer Pathology44
Correction: Regional Glymphatic Abnormality in Behavioral Variant Frontotemporal Dementia44
Correction: GATA1‐Mediated Transcriptional Regulation of the γ‐Secretase Activating Protein Increases Aβ Formation in Down Syndrome42
Visual Features in Stereo‐Electroencephalography to Predict Surgical Outcome: A Multicenter Study41
Ultrastructural Axon–Myelin Unit Alterations in Multiple Sclerosis Correlate with Inflammation41
Regional Brain Metabolism across the Alzheimer's Disease Continuum in Down Syndrome40
Dopamine Transporter Imaging as Objective Monitoring Biomarker in Parkinson's Disease40
Subicular Caspase‐1 Contributes to Pharmacoresistance in Temporal Lobe Epilepsy40
Trials for Slowly Progressive Neurogenetic Diseases Need Surrogate Endpoints39
GABRA1‐Related Disorders: From Genetic to Functional Pathways38
Development of Parkinson Disease and Its Relationship with Incidentally Discovered White Matter Disease and Covert Brain Infarction in a Real‐World Cohort38
Choroid Plexus Enlargement Exacerbates White Matter Hyperintensity Growth through Glymphatic Impairment37
Intravenous Thrombolysis in Patients Taking Direct Oral Anticoagulation Treatment Before Stroke Onset: Results from the Safe Implementations of Treatments in Stroke International Stroke Registry37
Association of Seizure Control with Mortality, Cognition, and Function in People With Dementia37
A Combined Panel of Salivary Biomarkers in de novo Parkinson's Disease37
Annals of Neurology: Volume 90, Number 3, September 202137
GGC Repeat Expansion of RILPL1 is Associated with Oculopharyngodistal Myopathy37
Improving Early Recognition of Treatment‐Responsive Causes of Rapidly Progressive Dementia: The STAM3P Score37
Issue Information36
COVID‐19‐Associated Critical Illness Myopathy with Direct Viral Effects36
Neuroimaging Biomarkers for Friedreich Ataxia: A Cross‐Sectional Analysis of the TRACKFA Study36
Actigraphy Enables Home Screening of Rapid Eye Movement Behavior Disorder in Parkinson's Disease36
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Bilateral Hearing Loss Caused by Inferior Collicular Infarction35
Reply to “Clinical Relevance of Genetic Variants in Juvenile Stroke Patients: A Plea for a Precise Classification”35
Reply to “Letter on Multiple Acyl‐Coenzyme A Dehydrogenase Deficiency Is Associated with Sertraline Use”35
NINDS Corner: The Helping to End Addiction Long‐Term Initiative and Pain Neurology35
Brain Iron Dysregulation in Iron Deficiency Anemia‐Related Restless Leg Syndrome Revealed by Neuron‐Derived Extracellular Vesicles: A Case–Control Study35
Promise of Nucleic Acid Therapeutics for Amyotrophic Lateral Sclerosis35
Is there an Association between Tuber Involvement of the Fusiform Face Area in Autism Diagnosis?34
Reply to “Is There an Association between Tuber Involvement of the Fusiform Face Area in Autism Diagnosis?”34
Nocturnal Pulse Event Frequency Is Reduced in Multiple System Atrophy34
Genome‐Wide Analysis of Structural Variants in Parkinson Disease34
Typical Radiological Features of a Rare Lateral Ventricular Liponeurocytoma34
Reply to “Chance Bias Arising from TSC2 Mutation Imbalance in the PREVeNT Trial”33
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Fighting Amyotrophic Lateral Sclerosis by Protecting the Liver? A Prospective Cohort Study33
Recessive Variants in PIGG Cause a Motor Neuropathy with Variable Conduction Block, Childhood Tremor, and Febrile Seizures: Expanding the Phenotype33
Issue Information33
Issue Information33
Prophylactic Fetal Creatine Supplementation Improves Post‐Asphyxial EEG Recovery and Reduces Seizures in Fetal Sheep: Implications for Hypoxic–Ischemic Encephalopathy33
Trigeminal Trophic Syndrome from Lateral Medullary Stroke33
Stage‐Dependent Biomarker Changes in Spinocerebellar Ataxia Type 332
Histopathological Correlates of Lobar Microbleeds in False‐Positive Cerebral Amyloid Angiopathy Cases32
Responsiveness of the Scale for the Assessment and Rating of Ataxia and Natural History in 884 Recessive and Early Onset Ataxia Patients32
Signs of Cortical Inflammation in Migraine Measured with Quantitative Magnetic Resonance Imaging: A Registry for Migraine (REFORM) Study32
High‐Dose Pulse Glucocorticoid Treatment Prevents White Matter Spinal Cord Pseudoatrophy in Newly Diagnosed Multiple Sclerosis32
Bleeding Risk of Dual Antiplatelet Therapy after Minor Stroke or Transient Ischemic Attack32
Greater Diffusion Restriction in White Matter in Preclinical Alzheimer Disease32
Compensated Hypogonadism Identified in Males with Cluster Headache: A Prospective Case‐Controlled Study32
Uncovering Image‐Driven Subtypes with Distinct Pathology and Clinical Course in Autopsy‐Confirmed Four Repeat Tauopathies31
Autoimmune Glial Fibrillary Acidic Protein Astrocytopathy Is Associated with HLA‐A*3303 and HLA‐DPB1*050131
Pathogenic MAST3 Variants in the STK Domain Are Associated with Epilepsy31
Seizures after Ischemic Stroke: A Matched Multicenter Study31
Automated Neuroprognostication Via Machine Learning in Neonates with Hypoxic‐Ischemic Encephalopathy31
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Determinants of Infarct Core Growth During Inter‐hospital Transfer for Thrombectomy30
Issue Information30
In Memoriam: Arthur Knight Asbury, MD (1928–2022)30
Issue Information – TOC30
ANA Investigates: Atrial Fibrillation after Stroke30
Correction: Decreased Cerebrospinal Fluid Amyloid β 38, 40, 42, and 43 Levels in Sporadic and Hereditary Cerebral Amyloid Angiopathy30
Issue Information30
Cerebral Small Vessel Disease Progression Increases Risk of Incident Parkinsonism29
Search Strategies for Alzheimer Protector Genes29
Adolescent Headache Due to Congenital Pelvic/Sacral Vascular Malformation29
Pivotal Role of Slitrk1 in Adult Striatal Cholinergic Neurons in Mice: Implication in Tourette Syndrome29
ANA Podcasts & Webinars: Genetics of Epilepsy29
Subcortical Volumes as Early Predictors of Fatigue in Multiple Sclerosis29
Extra Movements in Healthy People: Challenging the Definition and Diagnostic Practice of Tic Disorders29
Disease‐Modifying Drugs Extend Survival in Hereditary Transthyretin Amyloid Polyneuropathy28
Impact of Time of Day and Season on Outcome in Acute Ischemic Stroke28
Evaluation of Soluble Colony Stimulating Factor 1 Receptor (CSF1R) in Peripheral Blood as a Diagnostic Marker of CSF1R‐Related Disorder (CSF1RRD) in a Muri28
Reply to “VAERS Could Miss or Misinterpret Neurological Side Effects of COVID Vaccinations”28
Effect of Cumulative Exposure to Ocrelizumab on Memory B‐Cell Repopulation Dynamics in Multiple Sclerosis28
Risk of Multiple Sclerosis in People Living with HIV: An International Cohort Study28
SRPK3 Is Essential for Cognitive and Ocular Development in Humans and Zebrafish, Explaining X‐Linked Intellectual Disability27
Comparative Safety of Antiseizure Medication Monotherapy for Major Malformations27
Spoken Language Alterations can Predict Phenoconversion in Isolated Rapid Eye Movement Sleep Behavior Disorder: A Multicenter Study27
Application of the Amyloid/Tau/Neurodegeneration Framework in Cognitively Intact Adults: The CABLE Study27
Smouldering‐Associated Worsening in Multiple Sclerosis: An International Consensus Statement on Definition, Biology, Clinical Implications, and Future Directions27
Cortical Correlates of Gait Compensation Strategies in Parkinson Disease27
Ultra‐Low Level Somatic Mutations and Structural Variations in Focal Cortical Dysplasia Type II27
CADASIL Affects Multiple Aspects of Cerebral Small Vessel Function on 7T‐MRI27
Correction to Lyden P, Pryor KE, Coffey CS, et al. Final results of the RHAPSODY trial: a multi‐center, phase 2 trial using a continual reassessment method to determine the safety and toler26
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Annals of Neurology: Volume 95, Number 4, April 202426
Issue Information26
NORSE, FIRES, and a Polygenic Trickle of Autoimmunity26
Issue Information26
Annals of Neurology: Volume 96, Number 2, August 202426
Annual Report from the Editor‐in‐Chief (2024)26
Issue Information26
Neutrophils Are Associated with Higher Risk of Incident Amyotrophic Lateral Sclerosis in a BMI‐ and Age‐Dependent Manner25
Cinematic Rendering of Extracranial to Intracranial Arterial Bypass25
Vessel Wall Imaging of a Carotid Web25
Brainstem Ischemic Syndrome in NF2‐Related Schwannomatosis25
Internal Carotid Artery Pseudoaneurysm and Unilateral Vocal Cord Paralysis Secondary to Parapharyngeal Space Abscess25
Insular Stimulation Produces Mental Clarity and Bliss25
Emerging Management Challenges Posed by Atrial Fibrillation Detected After Stroke25
Sex Differences in Trends in Stroke Recurrence and Postrecurrence Mortality 2000–2020: Population‐Based Brain Attack Surveillance in Corpus Christi Project25
“Don't Throw the Baby out with the Bathwater”25
Social Health and Cognitive Change in Old Age: Role of Brain Reserve24
Fixating with the Paretic Eye: Evidence of “Fixation Duress” on PET Imaging24
Activated Wake Systems in Narcolepsy Type 124
Temporal Pattern of Cortical Hypoxia in Multiple Sclerosis and Its Significance on Neuropsychological and Clinical Measures of Disability24
Intravenous Thrombolysis with Tenecteplase for the Treatment of Acute Ischemic Stroke24
Disease Characteristics and Treatments Associated with Outcome in Primary Angiitis of the Central Nervous System—A Multicenter Cohort Study in 163 Patients24
A Carotid Web with Atherosclerotic Plaque24
Association of Apolipoprotein E ɛ4 Allele with Enlarged Perivascular Spaces24
Inflammation in Cerebral Amyloid Angiopathy‐Related Transient Focal Neurological Episodes24
Charcot Joint24
Disease Progression in Charcot–Marie–Tooth Disease Related to MPZ Mutations: A Longitudinal Study23
De Novo Missense Variants in SLC32A1 Cause a Developmental and Epileptic Encephalopathy Due to Impaired GABAergic Neurotransmission23
Diagnosing Epilepsy with Normal Interictal EEG Using Dynamic Network Models23
Systemic Metabolic Alteration Dependent on the Thyroid‐Liver Axis in Early PD23
Limbic Stimulation Drives Mania in STN‐DBS in Parkinson Disease: A Prospective Study23
High Levels of Perivascular Inflammation and Active Demyelinating Lesions at Time of Death Associated with Rapidly Progressive Multiple Sclerosis Disease Course: A Retrospective Postmortem Cohort Stud23
Role of the Exposome in Neurodegenerative Disease: Recent Insights and Future Directions23
Non–Cell Autonomous Epileptogenesis in Focal Cortical Dysplasia23
Salivary CGRP and Erenumab Treatment Response: Towards Precision Medicine in Migraine23
Longitudinal Alterations of Cerebral Blood Flow in High‐Contact Sports22
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Network Localization of Pediatric Lesion‐Induced Dystonia22
Cinematic Rendering of Twig‐Like Middle Cerebral Artery22
Annals of Neurology: Volume 92, Number 3, September 202222
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Issue Information22
Prediction of Cognitive Heterogeneity in Parkinson's Disease: A 4‐Year Longitudinal Study Using Clinical, Neuroimaging, Biological and Electrophysiological Biomarkers22
Blood‐Based Proteomics for Adult‐Onset Focal Dystonias21
Fostering Academia‐Industry Partnerships to Facilitate Therapeutic Discoveries in Neurology: The Role of ANA as a Catalyst21
MuSK‐Myasthenia Gravis and Cancer21
Enhancement of Glutamate Uptake as Novel Antiseizure Approach: Preclinical Proof of Concept21
Genetically Determined Low‐Density Lipoprotein Cholesterol and Risk of Subarachnoid Hemorrhage21
Reply to “Myelin Oligodendrocyte Glycoprotein Antibody‐Positive Patients Meeting the 2017 McDonald Criteria for Multiple Sclerosis: Challenges in Diagnosis and Treatment Decisions”21
Life‐Limiting Peripheral Organ Dysfunction in Feline Sandhoff Disease Emerges after Effective CNS Gene Therapy21
MOG‐IgG‐Associated Bilateral Optic Neuritis in Temporal Relation to Monkeypox Vaccination21
Ablating the Transporter Sodium‐Dependent Dicarboxylate Transporter 3 Prevents Leukodystrophy in Canavan Disease Mice21
Cognitive Effects of Deep Brain Stimulation in GBA‐Related Parkinson Disease21
Myelin Oligodendrocyte Glycoprotein Antibody‐Positive Patients Meeting the 2017 McDonald Criteria for Multiple Sclerosis: Challenges in Diagnosis and Treatment Decisions20
Re‐Emergence of Poliovirus in the United States: Considerations and Implications20
Cluster Headache Genomewide Association Study and Meta‐Analysis Identifies Eight Loci and Implicates Smoking as Causal Risk Factor20
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Decoding the Clinical Features that Associate with Progression, Causes, and Outcomes in Patients with Suspected Rapidly Progressive Dementia20
Levodopa Impairs the Energy Metabolism of the Basal Ganglia In Vivo20
Divergent Causes and Convergent Mechanisms of SUDEP20
Timing of Changes in Alzheimer's Disease Plasma Biomarkers as Assessed by Amyloid and Tau PET Clocks20
Neuroprotection of Low‐Frequency Repetitive Transcranial Magnetic Stimulation after Ischemic Stroke in Rats19
APOE Antibody Inhibits Aβ‐Associated Tau Seeding and Spreading in a Mouse Model19
Intact HIV Proviruses Persist in the Brain Despite Viral Suppression with ART19
Postictal Psychosis in Epilepsy: A Clinicogenetic Study19
Networks Underlie Temporal Onset of Dysplasia‐Related Epilepsy: A MELD Study19
Microglial and Astrocytic Responses in the Human Midcingulate Cortex in Huntington's Disease19
Proteomic Indicators of Health Predict Alzheimer's Disease Biomarker Levels and Dementia Risk19
Hydroxychloroquine for Primary Progressive Multiple Sclerosis19
AI in Neurology: Everything, Everywhere, All at Once Part 3: Surveillance, Synthesis, Simulation, and Systems19
Pragmatic Clinical Trials in Neurology19
Autosomal Recessive Cerebellar Ataxias: Translating Genes to Therapies18
Spasticity Predicts Motor Recovery for Patients with Subacute Motor Complete Spinal Cord Injury18
Reply to “Letter to the Editor, Regarding ‘Intravenous Thrombolysis in Patients Taking Direct Oral Anticoagulation Treatment Before Stroke Onset: Results from the Safe Implementations of Treatments in18
Disparate Dementia Risk Factors Are Associated with Cognitive Impairment and Rates of Decline in African Americans18
Annals of Neurology: Volume 93, Number 4, April 202318
Phase 1 Evaluation of Elezanumab (Anti–Repulsive Guidance Molecule A Monoclonal Antibody) in Healthy and Multiple Sclerosis Participants18
Annals of Neurology: Volume 90, Number 6, December 202118
Annals of Neurology: Volume 95, Number 3, March 202418
Divergent Associations of Slow‐Wave Sleep versus Rapid Eye Movement Sleep with Plasma Amyloid‐Beta18
Dominant KPNA3 Mutations Cause Infantile‐Onset Hereditary Spastic Paraplegia18
Presynaptic Dopaminergic Imaging Characterizes Patients with REM Sleep Behavior Disorder Due to Synucleinopathy18
Inhibition of Bone Morphogenetic Protein Signaling Prevents Tau Pathology in iPSC Derived Neurons and PS19 Mice18
Longitudinal Retinal Changes in MOGAD18
Natural History of Leigh Syndrome: A Study of Disease Burden and Progression18
Cerebrospinal Fluid Analysis Post–COVID‐19 Is Not Suggestive of Persistent Central Nervous System Infection17
The Starry Cortex of Aβ‐Related Angiitis17
Cost‐Effectiveness of Endovascular Thrombectomy in Patients with Large Ischemic Stroke17
Association of Mismatch Profiles and Clinical Outcome from Endovascular Therapy in Large Infarct: A Post‐Hoc Analysis of the ANGELASPECT Trial17
Characterizing Frontal Lobe Seizure Semiology in Children17
Reply to “Type I IFN Signature in NOTCH1‐Related Leukoencephalopathy”17
Amyloid‐Related Imaging Abnormalities in the DIAN‐TU‐001 Trial of Gantenerumab and Solanezumab: Lessons from a Trial in Dominantly Inherited Alzheimer Disease17
Perimesencephalic Hemorrhage from A Superior Cerebellar Artery Dissection17
Thalamic Influence on Slow Wave Slope Renormalization During Sleep17
Obesity and Multiple Sclerosis Severity: A Mendelian Randomization Study17
Clinically Meaningful Magnetic Resonance Endpoints Sensitive to Preataxic Spinocerebellar Ataxia Types 1 and 317
Annals of Neurology: Volume 91, Number 2, February 202216
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Independent Confirmation16
Letter on Spasticity Predicts Motor Recovery in Motor Complete Spinal Cord Injury16
High Frequency of Cognitive and Behavioral Impairment in Amyotrophic Lateral Sclerosis Patients with SOD1 Pathogenic Variants16
Issue Information16
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Aberrant GAP43 Gene Expression Is Alzheimer Disease Pathology‐Specific16
In Vivo Assessment of Astrocyte Reactivity in Patients with Progressive Supranuclear Palsy16
Annals of Neurology: Volume 96, Number 5, November 202416
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Clinical Relevance of ‘Cap’ and ‘Track’ Development after Recent Small Subcortical Infarct16
Reply to Suvorexant for Preventing Alzheimer's Disease16
Dystrophinopathy Phenotypes and Modifying Factors in DMD Exon 45–55 Deletion16
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