Annals of Neurology

Papers
(The median citation count of Annals of Neurology is 3. The table below lists those papers that are above that threshold based on CrossRef citation counts [max. 250 papers]. The publications cover those that have been published in the past four years, i.e., from 2021-09-01 to 2025-09-01.)
ArticleCitations
Annals of Neurology: Volume 90, Number S27, October 2021189
Issue Information151
Efficacy and Safety of Ofatumumab Treatment for Anti‐NMDA Receptor Autoimmune Encephalitis (OFFAE): A Prospective, Multicenter Cohort Study137
Elevated Cerebrospinal Fluid Ubiquitin Carboxyl‐Terminal Hydrolase Isozyme L1 in Asymptomatic C9orf72 Hexanucleotide Repeat Expansion Carriers129
Issue Information114
Carotid Stent Fracture104
Annals of Neurology: Volume 97, Number 1, January 2025104
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Supratentorial Lymphocytic Inflammation with Parenchymal Perivascular Enhancement Responsive to Steroids: A Potentially Overlooked Diagnosis94
Before, during, and after: An Argument for Safety and Improved Outcome of Thrombolysis in Acute Ischemic Stroke with Direct Oral Anticoagulant Treatment90
MS‐Driven Metabolic Alterations Are Recapitulated in iPSC‐Derived Astrocytes87
Vertebral Artery Pseudoaneurysm: Novel Marker of Bow Hunter's Syndrome84
Hypoparathyroidism Associated with Vascular Centrum Semiovale Calcifications81
Furthering Female Faculty: An American Neurological Association/Association of University Professors of Neurology Perspective80
HLA Associations of Intrathecal IgG Production against Specific Viruses in Multiple Sclerosis79
Interactions between High Seroreactivity to Human Herpes Virus 6A and Epstein–Barr Virus in MS Development: A Presymptomatic Case–Control Study78
A Letter Concerning a Role for Blood–Brain Barrier Dysfunction in Delirium following Noncardiac Surgery in Older Adults77
A Managed Care System with Telemedicine Support for Neurological Emergencies74
Cerebrospinal Fluid Flow in Patients with Huntington's Disease74
Cortical Microhemorrhage Presentation of Small Vessel Primary Angiitis of the Central Nervous System74
Network Localization of Awareness in Visual and Motor Anosognosia73
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Septin‐5 and ‐7‐IgGs: Neurologic, Serologic, and Pathophysiologic Characteristics69
The Use of Antihypertensive Medication and In Vivo Alzheimer's Disease Pathology63
Association of Retromer Deficiency and Tau Pathology in Down Syndrome63
Staufen Impairs Autophagy in Neurodegeneration60
Guanylate Kinase 1 Deficiency: A Novel and Potentially Treatable Mitochondrial DNA Depletion/Deletions Disease58
Prevalence of Cerebral Amyloid Angiopathy and Associated Risk of Subsequent Ischemic and Hemorrhagic Stroke and Mortality in a Nationwide Cohort57
Effect of Imaging Markers on Reperfusion Therapy in Basilar Artery Occlusion57
Plasma Metabolites Link Dietary Patterns to Stroke Risk57
Management of Cerebral Venous Thrombosis Due to Adenoviral COVID‐19 Vaccination57
Biological Age Acceleration and Motoric Cognitive Risk Syndrome56
Dysregulation of Gut Microbiota‐Derived Neuromodulatory Amino Acid Metabolism in Human Immunodeficiency Virus‐Associated Neurocognitive Disorder: An Integrative Metagenomic and Metabolomic 55
Severity of GNAO1‐Related Disorder Correlates with Changes in G‐Protein Function51
Blood Pressure after Successful Endovascular Therapy: A Systematic Review and Meta‐Analysis of Randomized Control Trials51
Epidemiology, Survival, and Clinical Characteristics of Inclusion Body Myositis50
A Role for Insulin‐like Growth Factor 1 in the Generation of Epileptic Spasms in a murine model50
Probabilistic Mapping Reveals Optimal Stimulation Site in Essential Tremor50
Reply to “Urinary α‐Synuclein for Parkinson's Detection: Key Limitations and Future Directions”50
Diet, Pace of Biological Aging, and Risk of Dementia in the Framingham Heart Study49
Suvorexant Acutely Decreases Tau Phosphorylation and Aβ in the Human CNS48
Annals of Neurology: Volume 94, Number S30, September 202348
Cover Image45
Annals of Neurology: Volume 90, Number S26, September 202145
Issue Information45
Micro‐Doses of DNP Preserve Motor and Muscle Function with a Period of Functional Recovery in Amyotrophic Lateral Sclerosis Mice43
Sports Concussion and Category Mistakes42
APOE2 Exacerbates TDP‐43 Related Toxicity in the Absence of Alzheimer Pathology42
Illusions of Self‐Motion during Magnetic Resonance‐Guided Focused Ultrasound Thalamotomy for Tremor42
RAN Translation of C9orf72‐Related Dipeptide Repeat Proteins in Zebrafish Recapitulates Hallmarks of Amyotrophic Lateral Sclerosis and Identifies Hypothermia as a Therapeutic Strategy42
Reply to “Core Penumbral Mismatch: An Independent Predictor of Stroke Poorer Outcome”42
MEK Pathway Inhibitor‐Mediated Response in BRAF V600‐Mutant Melanoma with Brain Parenchymal and Leptomeningeal Metastases42
A Combined Panel of Salivary Biomarkers in de novo Parkinson's Disease41
Longitudinal Imaging Biomarkers Correlate with Progressive Motor Deficit in the Mouse Model of Charlevoix‐Saguenay Ataxia41
Improving Early Recognition of Treatment‐Responsive Causes of Rapidly Progressive Dementia: The STAM3P Score41
Correction: GATA1‐Mediated Transcriptional Regulation of the γ‐Secretase Activating Protein Increases Aβ Formation in Down Syndrome40
Correction: Regional Glymphatic Abnormality in Behavioral Variant Frontotemporal Dementia40
Ultrastructural Axon–Myelin Unit Alterations in Multiple Sclerosis Correlate with Inflammation39
GGC Repeat Expansion of RILPL1 is Associated with Oculopharyngodistal Myopathy39
Tenascin‐R Autoimmunity: Isolated Tremor Reversed with Immunotherapy38
Regional Brain Metabolism across the Alzheimer's Disease Continuum in Down Syndrome38
Intravenous Thrombolysis in Patients Taking Direct Oral Anticoagulation Treatment Before Stroke Onset: Results from the Safe Implementations of Treatments in Stroke International Stroke Registry38
GABRA1‐Related Disorders: From Genetic to Functional Pathways38
Dopamine Transporter Imaging as Objective Monitoring Biomarker in Parkinson's Disease37
Trials for Slowly Progressive Neurogenetic Diseases Need Surrogate Endpoints37
Issue Information37
Association of Seizure Control with Mortality, Cognition, and Function in People With Dementia37
Visual Features in Stereo‐Electroencephalography to Predict Surgical Outcome: A Multicenter Study37
Development of Parkinson Disease and Its Relationship with Incidentally Discovered White Matter Disease and Covert Brain Infarction in a Real‐World Cohort36
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Choroid Plexus Enlargement Exacerbates White Matter Hyperintensity Growth through Glymphatic Impairment36
Issue Information36
Annals of Neurology: Volume 90, Number 3, September 202136
Brain Iron Dysregulation in Iron Deficiency Anemia‐Related Restless Leg Syndrome Revealed by Neuron‐Derived Extracellular Vesicles: A Case–Control Study35
Nocturnal Pulse Event Frequency Is Reduced in Multiple System Atrophy35
Bilateral Hearing Loss Caused by Inferior Collicular Infarction35
Reply to “Clinical Relevance of Genetic Variants in Juvenile Stroke Patients: A Plea for a Precise Classification”35
Is there an Association between Tuber Involvement of the Fusiform Face Area in Autism Diagnosis?35
Reply to “Letter on Multiple Acyl‐Coenzyme A Dehydrogenase Deficiency Is Associated with Sertraline Use”35
NINDS Corner: The Helping to End Addiction Long‐Term Initiative and Pain Neurology35
Typical Radiological Features of a Rare Lateral Ventricular Liponeurocytoma35
Issue Information34
Promise of Nucleic Acid Therapeutics for Amyotrophic Lateral Sclerosis34
High‐Dose Pulse Glucocorticoid Treatment Prevents White Matter Spinal Cord Pseudoatrophy in Newly Diagnosed Multiple Sclerosis34
Reply to “Chance Bias Arising from TSC2 Mutation Imbalance in the PREVeNT Trial”34
Bleeding Risk of Dual Antiplatelet Therapy after Minor Stroke or Transient Ischemic Attack34
Reply to “Is There an Association between Tuber Involvement of the Fusiform Face Area in Autism Diagnosis?”34
Issue Information33
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Trigeminal Trophic Syndrome from Lateral Medullary Stroke33
Histopathological Correlates of Lobar Microbleeds in False‐Positive Cerebral Amyloid Angiopathy Cases32
Prophylactic Fetal Creatine Supplementation Improves Post‐Asphyxial EEG Recovery and Reduces Seizures in Fetal Sheep: Implications for Hypoxic–Ischemic Encephalopathy32
Compensated Hypogonadism Identified in Males with Cluster Headache: A Prospective Case‐Controlled Study32
Recessive Variants in PIGG Cause a Motor Neuropathy with Variable Conduction Block, Childhood Tremor, and Febrile Seizures: Expanding the Phenotype32
Signs of Cortical Inflammation in Migraine Measured with Quantitative Magnetic Resonance Imaging: A Registry for Migraine (REFORM) Study32
Determinants of Infarct Core Growth During Inter‐hospital Transfer for Thrombectomy31
Use of FDGPET in Balamuthia mandrillaris Amebic Encephalitis31
Stage‐Dependent Biomarker Changes in Spinocerebellar Ataxia Type 331
Neuroimaging Biomarkers for Friedreich Ataxia: A Cross‐Sectional Analysis of the TRACKFA Study31
Autoimmune Glial Fibrillary Acidic Protein Astrocytopathy Is Associated with HLA‐A*3303 and HLA‐DPB1*050131
Heart Rate Profiles During Exercise and Incident Parkinson's Disease31
Responsiveness of the Scale for the Assessment and Rating of Ataxia and Natural History in 884 Recessive and Early Onset Ataxia Patients30
Fighting Amyotrophic Lateral Sclerosis by Protecting the Liver? A Prospective Cohort Study30
Actigraphy Enables Home Screening of Rapid Eye Movement Behavior Disorder in Parkinson's Disease30
Seizures after Ischemic Stroke: A Matched Multicenter Study30
Genome‐Wide Analysis of Structural Variants in Parkinson Disease30
Greater Diffusion Restriction in White Matter in Preclinical Alzheimer Disease30
Automated Neuroprognostication Via Machine Learning in Neonates with Hypoxic‐Ischemic Encephalopathy30
In Memoriam: Arthur Knight Asbury, MD (1928–2022)30
COVID‐19‐Associated Critical Illness Myopathy with Direct Viral Effects30
Uncovering Image‐Driven Subtypes with Distinct Pathology and Clinical Course in Autopsy‐Confirmed Four Repeat Tauopathies30
SRPK3 Is Essential for Cognitive and Ocular Development in Humans and Zebrafish, Explaining X‐Linked Intellectual Disability29
Issue Information29
Correction: Decreased Cerebrospinal Fluid Amyloid β 38, 40, 42, and 43 Levels in Sporadic and Hereditary Cerebral Amyloid Angiopathy29
Cerebral Small Vessel Disease Progression Increases Risk of Incident Parkinsonism29
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Issue Information – TOC29
Pivotal Role of Slitrk1 in Adult Striatal Cholinergic Neurons in Mice: Implication in Tourette Syndrome29
ANA Investigates: Atrial Fibrillation after Stroke29
Issue Information29
Evaluation of Soluble Colony Stimulating Factor 1 Receptor (CSF1R) in Peripheral Blood as a Diagnostic Marker of CSF1R‐Related Disorder (CSF1RRD) in a Muri28
Adolescent Headache Due to Congenital Pelvic/Sacral Vascular Malformation28
ANA Podcasts & Webinars: Genetics of Epilepsy28
Application of the Amyloid/Tau/Neurodegeneration Framework in Cognitively Intact Adults: The CABLE Study28
Disease‐Modifying Drugs Extend Survival in Hereditary Transthyretin Amyloid Polyneuropathy28
Risk of Multiple Sclerosis in People Living with HIV: An International Cohort Study28
Search Strategies for Alzheimer Protector Genes28
Elevated Risk of Cerebral Arteriovenous Malformation Rupture during Pregnancy and Puerperium27
Subcortical Volumes as Early Predictors of Fatigue in Multiple Sclerosis27
Reply to “VAERS Could Miss or Misinterpret Neurological Side Effects of COVID Vaccinations”27
CADASIL Affects Multiple Aspects of Cerebral Small Vessel Function on 7T‐MRI27
Effect of Cumulative Exposure to Ocrelizumab on Memory B‐Cell Repopulation Dynamics in Multiple Sclerosis27
Extra Movements in Healthy People: Challenging the Definition and Diagnostic Practice of Tic Disorders27
Ultra‐Low Level Somatic Mutations and Structural Variations in Focal Cortical Dysplasia Type II27
Spoken Language Alterations can Predict Phenoconversion in Isolated Rapid Eye Movement Sleep Behavior Disorder: A Multicenter Study27
Cortical Correlates of Gait Compensation Strategies in Parkinson Disease26
Issue Information26
Smouldering‐Associated Worsening in Multiple Sclerosis: An International Consensus Statement on Definition, Biology, Clinical Implications, and Future Directions26
Annals of Neurology: Volume 96, Number 2, August 202426
Issue Information26
Comparative Safety of Antiseizure Medication Monotherapy for Major Malformations26
Issue Information26
Annals of Neurology: Volume 95, Number 4, April 202426
NORSE, FIRES, and a Polygenic Trickle of Autoimmunity25
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Brainstem Ischemic Syndrome in NF2‐Related Schwannomatosis25
Annual Report from the Editor‐in‐Chief (2024)25
Emerging Management Challenges Posed by Atrial Fibrillation Detected After Stroke25
Correction to Lyden P, Pryor KE, Coffey CS, et al. Final results of the RHAPSODY trial: a multi‐center, phase 2 trial using a continual reassessment method to determine the safety and toler25
Neutrophils Are Associated with Higher Risk of Incident Amyotrophic Lateral Sclerosis in a BMI‐ and Age‐Dependent Manner25
Cinematic Rendering of Extracranial to Intracranial Arterial Bypass25
Trametinib in Adults with Neurofibromatosis Type 1‐Related Symptomatic Plexiform Neurofibromas24
A Carotid Web with Atherosclerotic Plaque24
Sex Differences in Trends in Stroke Recurrence and Postrecurrence Mortality 2000–2020: Population‐Based Brain Attack Surveillance in Corpus Christi Project24
Insular Stimulation Produces Mental Clarity and Bliss24
Social Health and Cognitive Change in Old Age: Role of Brain Reserve24
Internal Carotid Artery Pseudoaneurysm and Unilateral Vocal Cord Paralysis Secondary to Parapharyngeal Space Abscess24
Polygenic Resistance to Blood Pressure Treatment and Stroke Risk: Insights from the All of Us Research Program24
Temporal Pattern of Cortical Hypoxia in Multiple Sclerosis and Its Significance on Neuropsychological and Clinical Measures of Disability24
Vessel Wall Imaging of a Carotid Web24
Disease Characteristics and Treatments Associated with Outcome in Primary Angiitis of the Central Nervous System—A Multicenter Cohort Study in 163 Patients23
Limbic Stimulation Drives Mania in STN‐DBS in Parkinson Disease: A Prospective Study23
Intravenous Thrombolysis with Tenecteplase for the Treatment of Acute Ischemic Stroke23
Charcot Joint23
Fixating with the Paretic Eye: Evidence of “Fixation Duress” on PET Imaging23
High Levels of Perivascular Inflammation and Active Demyelinating Lesions at Time of Death Associated with Rapidly Progressive Multiple Sclerosis Disease Course: A Retrospective Postmortem Cohort Stud23
Systemic Metabolic Alteration Dependent on the Thyroid‐Liver Axis in Early PD23
“Don't Throw the Baby out with the Bathwater”23
Prediction of Cognitive Heterogeneity in Parkinson's Disease: A 4‐Year Longitudinal Study Using Clinical, Neuroimaging, Biological and Electrophysiological Biomarkers22
Association of Apolipoprotein E ɛ4 Allele with Enlarged Perivascular Spaces22
Disease Progression in Charcot–Marie–Tooth Disease Related to MPZ Mutations: A Longitudinal Study22
Diagnosing Epilepsy with Normal Interictal EEG Using Dynamic Network Models22
Network Localization of Pediatric Lesion‐Induced Dystonia22
Salivary CGRP and Erenumab Treatment Response: Towards Precision Medicine in Migraine22
De Novo Missense Variants in SLC32A1 Cause a Developmental and Epileptic Encephalopathy Due to Impaired GABAergic Neurotransmission22
Inflammation in Cerebral Amyloid Angiopathy‐Related Transient Focal Neurological Episodes22
Issue Information21
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Role of the Exposome in Neurodegenerative Disease: Recent Insights and Future Directions21
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Activated Wake Systems in Narcolepsy Type 121
Annals of Neurology: Volume 92, Number 3, September 202221
Cinematic Rendering of Twig‐Like Middle Cerebral Artery20
Enhancement of Glutamate Uptake as Novel Antiseizure Approach: Preclinical Proof of Concept20
Intact HIV Proviruses Persist in the Brain Despite Viral Suppression with ART20
MOG‐IgG‐Associated Bilateral Optic Neuritis in Temporal Relation to Monkeypox Vaccination20
Fostering Academia‐Industry Partnerships to Facilitate Therapeutic Discoveries in Neurology: The Role of ANA as a Catalyst20
Spasticity Predicts Motor Recovery for Patients with Subacute Motor Complete Spinal Cord Injury20
Proteomic Indicators of Health Predict Alzheimer's Disease Biomarker Levels and Dementia Risk20
Life‐Limiting Peripheral Organ Dysfunction in Feline Sandhoff Disease Emerges after Effective CNS Gene Therapy20
Pragmatic Clinical Trials in Neurology20
Reply to “Myelin Oligodendrocyte Glycoprotein Antibody‐Positive Patients Meeting the 2017 McDonald Criteria for Multiple Sclerosis: Challenges in Diagnosis and Treatment Decisions”19
Ablating the Transporter Sodium‐Dependent Dicarboxylate Transporter 3 Prevents Leukodystrophy in Canavan Disease Mice19
Hydroxychloroquine for Primary Progressive Multiple Sclerosis19
AI in Neurology: Everything, Everywhere, All at Once Part 3: Surveillance, Synthesis, Simulation, and Systems19
MuSK‐Myasthenia Gravis and Cancer19
Divergent Causes and Convergent Mechanisms of SUDEP19
Cluster Headache Genomewide Association Study and Meta‐Analysis Identifies Eight Loci and Implicates Smoking as Causal Risk Factor19
Decoding the Clinical Features that Associate with Progression, Causes, and Outcomes in Patients with Suspected Rapidly Progressive Dementia19
Cognitive Effects of Deep Brain Stimulation in GBA‐Related Parkinson Disease19
Blood‐Based Proteomics for Adult‐Onset Focal Dystonias19
Myelin Oligodendrocyte Glycoprotein Antibody‐Positive Patients Meeting the 2017 McDonald Criteria for Multiple Sclerosis: Challenges in Diagnosis and Treatment Decisions19
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Microglial and Astrocytic Responses in the Human Midcingulate Cortex in Huntington's Disease18
Autosomal Recessive Cerebellar Ataxias: Translating Genes to Therapies18
Annals of Neurology: Volume 95, Number 3, March 202418
Timing of Changes in Alzheimer's Disease Plasma Biomarkers as Assessed by Amyloid and Tau PET Clocks18
Networks Underlie Temporal Onset of Dysplasia‐Related Epilepsy: A MELD Study18
APOE Antibody Inhibits Aβ‐Associated Tau Seeding and Spreading in a Mouse Model18
Dominant KPNA3 Mutations Cause Infantile‐Onset Hereditary Spastic Paraplegia18
Re‐Emergence of Poliovirus in the United States: Considerations and Implications18
Disparate Dementia Risk Factors Are Associated with Cognitive Impairment and Rates of Decline in African Americans18
Annals of Neurology: Volume 93, Number 4, April 202318
Genetically Determined Low‐Density Lipoprotein Cholesterol and Risk of Subarachnoid Hemorrhage18
Longitudinal Alterations of Cerebral Blood Flow in High‐Contact Sports18
Reply to “Reassessing the Impact of Endovascular Thrombectomy on Cerebral Edema and Functional Outcomes”18
Neuroprotection of Low‐Frequency Repetitive Transcranial Magnetic Stimulation after Ischemic Stroke in Rats18
Phase 1 Evaluation of Elezanumab (Anti–Repulsive Guidance Molecule A Monoclonal Antibody) in Healthy and Multiple Sclerosis Participants18
Annals of Neurology: Volume 90, Number 6, December 202118
Presynaptic Dopaminergic Imaging Characterizes Patients with REM Sleep Behavior Disorder Due to Synucleinopathy18
Levodopa Impairs the Energy Metabolism of the Basal Ganglia In Vivo18
Reply to “Letter to the Editor, Regarding ‘Intravenous Thrombolysis in Patients Taking Direct Oral Anticoagulation Treatment Before Stroke Onset: Results from the Safe Implementations of Treatments in17
Perimesencephalic Hemorrhage from A Superior Cerebellar Artery Dissection17
The Starry Cortex of Aβ‐Related Angiitis17
Clinically Meaningful Magnetic Resonance Endpoints Sensitive to Preataxic Spinocerebellar Ataxia Types 1 and 317
Natural History of Leigh Syndrome: A Study of Disease Burden and Progression17
Reply to “Type I IFN Signature in NOTCH1‐Related Leukoencephalopathy”17
Thalamic Influence on Slow Wave Slope Renormalization During Sleep17
Mutations in CLCN6 as a Novel Genetic Cause of Neuronal Ceroid Lipofuscinosis in Patients and a Murine Model17
Eligibility Rates among Racially and Ethnically Diverse US Participants in Phase 2 and Phase 3 Placebo‐Controlled, Double‐Blind, Randomized Trials of Lecanemab and Elenbecestat in Early Alz17
Association of Mismatch Profiles and Clinical Outcome from Endovascular Therapy in Large Infarct: A Post‐Hoc Analysis of the ANGELASPECT Trial17
Divergent Associations of Slow‐Wave Sleep versus Rapid Eye Movement Sleep with Plasma Amyloid‐Beta17
Obesity and Multiple Sclerosis Severity: A Mendelian Randomization Study17
Cost‐Effectiveness of Endovascular Thrombectomy in Patients with Large Ischemic Stroke17
Amyloid‐Related Imaging Abnormalities in the DIAN‐TU‐001 Trial of Gantenerumab and Solanezumab: Lessons from a Trial in Dominantly Inherited Alzheimer Disease17
Proteomics and the Risk of Incident Embolic and Thrombotic Stroke17
Early Treatment with Vigabatrin Does Not Decrease Focal Seizures or Improve Cognition in Tuberous Sclerosis Complex: The PREVeNT Trial16
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Dystrophinopathy Phenotypes and Modifying Factors in DMD Exon 45–55 Deletion16
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Annals of Neurology: Volume 91, Number 2, February 202216
Annals of Neurology: Volume 96, Number 5, November 202416
Neurological Events Reported after COVID‐19 Vaccines: An Analysis of Vaccine Adverse Event Reporting System16
Characterizing Frontal Lobe Seizure Semiology in Children16
Issue Information16
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Mapping Molecular Pathways of Multiple Sclerosis: A Gene Prioritization and Network Analysis of White Matter Pathology Transcriptomics16
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