Annals of Neurology

Papers
(The TQCC of Annals of Neurology is 13. The table below lists those papers that are above that threshold based on CrossRef citation counts [max. 250 papers]. The publications cover those that have been published in the past four years, i.e., from 2021-06-01 to 2025-06-01.)
ArticleCitations
Annals of Neurology: Volume 90, Number S27, October 2021178
Issue Information164
Cortical Microhemorrhage Presentation of Small Vessel Primary Angiitis of the Central Nervous System140
Elevated Cerebrospinal Fluid Ubiquitin Carboxyl‐Terminal Hydrolase Isozyme L1 in Asymptomatic C9orf72 Hexanucleotide Repeat Expansion Carriers127
Issue Information124
Annals of Neurology: Volume 97, Number 1, January 2025115
Carotid Stent Fracture109
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Efficacy and Safety of Ofatumumab Treatment for Anti‐NMDA Receptor Autoimmune Encephalitis (OFFAE): A Prospective, Multicenter Cohort Study100
Vertebral Artery Pseudoaneurysm: Novel Marker of Bow Hunter's Syndrome94
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Prevalence of Cerebral Amyloid Angiopathy and Associated Risk of Subsequent Ischemic and Hemorrhagic Stroke and Mortality in a Nationwide Cohort93
Association of Retromer Deficiency and Tau Pathology in Down Syndrome91
Hypoparathyroidism Associated with Vascular Centrum Semiovale Calcifications91
A Role for Insulin‐like Growth Factor 1 in the Generation of Epileptic Spasms in a murine model90
Effect of Imaging Markers on Reperfusion Therapy in Basilar Artery Occlusion87
Septin‐5 and ‐7‐IgGs: Neurologic, Serologic, and Pathophysiologic Characteristics86
Supratentorial Lymphocytic Inflammation with Parenchymal Perivascular Enhancement Responsive to Steroids: A Potentially Overlooked Diagnosis78
Furthering Female Faculty: An American Neurological Association/Association of University Professors of Neurology Perspective77
Blood Pressure after Successful Endovascular Therapy: A Systematic Review and Meta‐Analysis of Randomized Control Trials77
HLA Associations of Intrathecal IgG Production against Specific Viruses in Multiple Sclerosis74
Interactions between High Seroreactivity to Human Herpes Virus 6A and Epstein–Barr Virus in MS Development: A Presymptomatic Case–Control Study72
A Letter Concerning a Role for Blood–Brain Barrier Dysfunction in Delirium following Noncardiac Surgery in Older Adults71
Cerebrospinal Fluid Flow in Patients with Huntington's Disease70
MS‐Driven Metabolic Alterations Are Recapitulated in iPSC‐Derived Astrocytes69
A Managed Care System with Telemedicine Support for Neurological Emergencies68
Biological Age Acceleration and Motoric Cognitive Risk Syndrome66
Severity of GNAO1‐Related Disorder Correlates with Changes in G‐Protein Function64
The Use of Antihypertensive Medication and In Vivo Alzheimer's Disease Pathology64
Staufen Impairs Autophagy in Neurodegeneration62
Human Brain Resilience: A Call to Action61
Before, during, and after: An Argument for Safety and Improved Outcome of Thrombolysis in Acute Ischemic Stroke with Direct Oral Anticoagulant Treatment61
Polygenic Risk Score for Alzheimer's Disease in Caribbean Hispanics60
Suvorexant Acutely Decreases Tau Phosphorylation and Aβ in the Human CNS56
Dysregulation of Gut Microbiota‐Derived Neuromodulatory Amino Acid Metabolism in Human Immunodeficiency Virus‐Associated Neurocognitive Disorder: An Integrative Metagenomic and Metabolomic 56
Probabilistic Mapping Reveals Optimal Stimulation Site in Essential Tremor54
Network Localization of Awareness in Visual and Motor Anosognosia53
Epidemiology, Survival, and Clinical Characteristics of Inclusion Body Myositis52
Management of Cerebral Venous Thrombosis Due to Adenoviral COVID‐19 Vaccination51
Guanylate Kinase 1 Deficiency: A Novel and Potentially Treatable Mitochondrial DNA Depletion/Deletions Disease51
Diet, Pace of Biological Aging, and Risk of Dementia in the Framingham Heart Study49
Annals of Neurology: Volume 94, Number S30, September 202347
Plasma Metabolites Link Dietary Patterns to Stroke Risk47
Annals of Neurology: Volume 90, Number S26, September 202146
Cover Image46
Issue Information45
Longitudinal Imaging Biomarkers Correlate with Progressive Motor Deficit in the Mouse Model of Charlevoix‐Saguenay Ataxia45
Micro‐Doses of DNP Preserve Motor and Muscle Function with a Period of Functional Recovery in Amyotrophic Lateral Sclerosis Mice45
Association of Seizure Control with Mortality, Cognition, and Function in People With Dementia44
Sports Concussion and Category Mistakes44
Illusions of Self‐Motion during Magnetic Resonance‐Guided Focused Ultrasound Thalamotomy for Tremor44
Tenascin‐R Autoimmunity: Isolated Tremor Reversed with Immunotherapy44
Reply to “Core Penumbral Mismatch: An Independent Predictor of Stroke Poorer Outcome”43
RAN Translation of C9orf72‐Related Dipeptide Repeat Proteins in Zebrafish Recapitulates Hallmarks of Amyotrophic Lateral Sclerosis and Identifies Hypothermia as a Therapeutic Strategy43
MEK Pathway Inhibitor‐Mediated Response in BRAF V600‐Mutant Melanoma with Brain Parenchymal and Leptomeningeal Metastases42
Regional Brain Metabolism across the Alzheimer's Disease Continuum in Down Syndrome41
Development of Parkinson Disease and Its Relationship with Incidentally Discovered White Matter Disease and Covert Brain Infarction in a Real‐World Cohort41
Correction: GATA1‐Mediated Transcriptional Regulation of the γ‐Secretase Activating Protein Increases Aβ Formation in Down Syndrome41
Correction: Regional Glymphatic Abnormality in Behavioral Variant Frontotemporal Dementia41
Improving Early Recognition of Treatment‐Responsive Causes of Rapidly Progressive Dementia: The STAM3P Score40
Trials for Slowly Progressive Neurogenetic Diseases Need Surrogate Endpoints40
GGC Repeat Expansion of RILPL1 is Associated with Oculopharyngodistal Myopathy39
Dopamine Transporter Imaging as Objective Monitoring Biomarker in Parkinson's Disease38
Subicular Caspase‐1 Contributes to Pharmacoresistance in Temporal Lobe Epilepsy38
Intravenous Thrombolysis in Patients Taking Direct Oral Anticoagulation Treatment Before Stroke Onset: Results from the Safe Implementations of Treatments in Stroke International Stroke Registry37
GABRA1‐Related Disorders: From Genetic to Functional Pathways37
Ultrastructural Axon–Myelin Unit Alterations in Multiple Sclerosis Correlate with Inflammation36
A Combined Panel of Salivary Biomarkers in de novo Parkinson's Disease36
APOE2 Exacerbates TDP‐43 Related Toxicity in the Absence of Alzheimer Pathology36
Choroid Plexus Enlargement Exacerbates White Matter Hyperintensity Growth through Glymphatic Impairment36
Annals of Neurology: Volume 90, Number 3, September 202135
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Issue Information35
Reply to “Clinical Relevance of Genetic Variants in Juvenile Stroke Patients: A Plea for a Precise Classification”35
Preservation of Brain Activity in Unresponsive Patients Identifies MCS Star35
Neuroimaging Biomarkers for Friedreich Ataxia: A Cross‐Sectional Analysis of the TRACKFA Study35
NINDS Corner: The Helping to End Addiction Long‐Term Initiative and Pain Neurology35
Reply to “Letter on Multiple Acyl‐Coenzyme A Dehydrogenase Deficiency Is Associated with Sertraline Use”34
Pathogenic MAST3 Variants in the STK Domain Are Associated with Epilepsy34
Brain Iron Dysregulation in Iron Deficiency Anemia‐Related Restless Leg Syndrome Revealed by Neuron‐Derived Extracellular Vesicles: A Case–Control Study34
Bilateral Hearing Loss Caused by Inferior Collicular Infarction34
Typical Radiological Features of a Rare Lateral Ventricular Liponeurocytoma33
Promise of Nucleic Acid Therapeutics for Amyotrophic Lateral Sclerosis33
Reply to “Chance Bias Arising from TSC2 Mutation Imbalance in the PREVeNT Trial”32
Is there an Association between Tuber Involvement of the Fusiform Face Area in Autism Diagnosis?32
Issue Information32
Genome‐Wide Analysis of Structural Variants in Parkinson Disease32
Fighting Amyotrophic Lateral Sclerosis by Protecting the Liver? A Prospective Cohort Study32
Compensated Hypogonadism Identified in Males with Cluster Headache: A Prospective Case‐Controlled Study32
Reply to “Is There an Association between Tuber Involvement of the Fusiform Face Area in Autism Diagnosis?”32
Issue Information32
Nocturnal Pulse Event Frequency Is Reduced in Multiple System Atrophy32
Trigeminal Trophic Syndrome from Lateral Medullary Stroke31
Signs of Cortical Inflammation in Migraine Measured with Quantitative Magnetic Resonance Imaging: A Registry for Migraine (REFORM) Study31
Bleeding Risk of Dual Antiplatelet Therapy after Minor Stroke or Transient Ischemic Attack31
Recessive Variants in PIGG Cause a Motor Neuropathy with Variable Conduction Block, Childhood Tremor, and Febrile Seizures: Expanding the Phenotype31
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Automated Neuroprognostication Via Machine Learning in Neonates with Hypoxic‐Ischemic Encephalopathy31
Prophylactic Fetal Creatine Supplementation Improves Post‐Asphyxial EEG Recovery and Reduces Seizures in Fetal Sheep: Implications for Hypoxic–Ischemic Encephalopathy31
Actigraphy Enables Home Screening of Rapid Eye Movement Behavior Disorder in Parkinson's Disease31
Stage‐Dependent Biomarker Changes in Spinocerebellar Ataxia Type 330
Greater Diffusion Restriction in White Matter in Preclinical Alzheimer Disease30
Responsiveness of the Scale for the Assessment and Rating of Ataxia and Natural History in 884 Recessive and Early Onset Ataxia Patients30
Autoimmune Glial Fibrillary Acidic Protein Astrocytopathy Is Associated with HLA‐A*3303 and HLA‐DPB1*050130
Seizures after Ischemic Stroke: A Matched Multicenter Study30
In Memoriam: Arthur Knight Asbury, MD (1928–2022)30
COVID‐19‐Associated Critical Illness Myopathy with Direct Viral Effects30
Histopathological Correlates of Lobar Microbleeds in False‐Positive Cerebral Amyloid Angiopathy Cases30
Determinants of Infarct Core Growth During Inter‐hospital Transfer for Thrombectomy30
Correction: Decreased Cerebrospinal Fluid Amyloid β 38, 40, 42, and 43 Levels in Sporadic and Hereditary Cerebral Amyloid Angiopathy30
Evaluation of Soluble Colony Stimulating Factor 1 Receptor (CSF1R) in Peripheral Blood as a Diagnostic Marker of CSF1R‐Related Disorder (CSF1RRD) in a Muri29
ANA Investigates: Atrial Fibrillation after Stroke29
Cerebral Small Vessel Disease Progression Increases Risk of Incident Parkinsonism29
Issue Information29
Issue Information – TOC29
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Issue Information29
Ultra‐Low Level Somatic Mutations and Structural Variations in Focal Cortical Dysplasia Type II29
Search Strategies for Alzheimer Protector Genes28
Risk of Multiple Sclerosis in People Living with HIV: An International Cohort Study28
ANA Podcasts & Webinars: Genetics of Epilepsy28
Disease‐Modifying Drugs Extend Survival in Hereditary Transthyretin Amyloid Polyneuropathy28
Adolescent Headache Due to Congenital Pelvic/Sacral Vascular Malformation28
Application of the Amyloid/Tau/Neurodegeneration Framework in Cognitively Intact Adults: The CABLE Study28
Pivotal Role of Slitrk1 in Adult Striatal Cholinergic Neurons in Mice: Implication in Tourette Syndrome27
Cortical Correlates of Gait Compensation Strategies in Parkinson Disease27
CADASIL Affects Multiple Aspects of Cerebral Small Vessel Function on 7T‐MRI27
Reply to “VAERS Could Miss or Misinterpret Neurological Side Effects of COVID Vaccinations”27
Spoken Language Alterations can Predict Phenoconversion in Isolated Rapid Eye Movement Sleep Behavior Disorder: A Multicenter Study27
Comparative Safety of Antiseizure Medication Monotherapy for Major Malformations27
SRPK3 Is Essential for Cognitive and Ocular Development in Humans and Zebrafish, Explaining X‐Linked Intellectual Disability27
Impact of Time of Day and Season on Outcome in Acute Ischemic Stroke27
Subcortical Volumes as Early Predictors of Fatigue in Multiple Sclerosis27
Extra Movements in Healthy People: Challenging the Definition and Diagnostic Practice of Tic Disorders27
Issue Information26
Annals of Neurology: Volume 96, Number 2, August 202426
NORSE, FIRES, and a Polygenic Trickle of Autoimmunity26
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Smouldering‐Associated Worsening in Multiple Sclerosis: An International Consensus Statement on Definition, Biology, Clinical Implications, and Future Directions26
Issue Information26
Issue Information26
Annual Report from the Editor‐in‐Chief (2024)26
Annals of Neurology: Volume 95, Number 4, April 202426
Issue Information26
Correction to Lyden P, Pryor KE, Coffey CS, et al. Final results of the RHAPSODY trial: a multi‐center, phase 2 trial using a continual reassessment method to determine the safety and toler26
Diagnosing Epilepsy with Normal Interictal EEG Using Dynamic Network Models26
Emerging Management Challenges Posed by Atrial Fibrillation Detected After Stroke25
Neutrophils Are Associated with Higher Risk of Incident Amyotrophic Lateral Sclerosis in a BMI‐ and Age‐Dependent Manner25
Activated Wake Systems in Narcolepsy Type 125
Brainstem Ischemic Syndrome in NF2‐Related Schwannomatosis25
Cinematic Rendering of Extracranial to Intracranial Arterial Bypass25
Social Health and Cognitive Change in Old Age: Role of Brain Reserve25
Internal Carotid Artery Pseudoaneurysm and Unilateral Vocal Cord Paralysis Secondary to Parapharyngeal Space Abscess25
Insular Stimulation Produces Mental Clarity and Bliss24
A Carotid Web with Atherosclerotic Plaque24
“Don't Throw the Baby out with the Bathwater”24
Prediction of Cognitive Heterogeneity in Parkinson's Disease: A 4‐Year Longitudinal Study Using Clinical, Neuroimaging, Biological and Electrophysiological Biomarkers24
Fixating with the Paretic Eye: Evidence of “Fixation Duress” on PET Imaging24
Vessel Wall Imaging of a Carotid Web24
High Levels of Perivascular Inflammation and Active Demyelinating Lesions at Time of Death Associated with Rapidly Progressive Multiple Sclerosis Disease Course: A Retrospective Postmortem Cohort Stud24
Limbic Stimulation Drives Mania in STN‐DBS in Parkinson Disease: A Prospective Study24
Systemic Metabolic Alteration Dependent on the Thyroid‐Liver Axis in Early PD24
Sex Differences in Trends in Stroke Recurrence and Postrecurrence Mortality 2000–2020: Population‐Based Brain Attack Surveillance in Corpus Christi Project24
Charcot Joint23
Intrathecal Immunoglobulin M Synthesis is an Independent Biomarker for Higher Disease Activity and Severity in Multiple Sclerosis23
Network Localization of Pediatric Lesion‐Induced Dystonia23
Temporal Pattern of Cortical Hypoxia in Multiple Sclerosis and Its Significance on Neuropsychological and Clinical Measures of Disability23
Salivary CGRP and Erenumab Treatment Response: Towards Precision Medicine in Migraine23
Non–Cell Autonomous Epileptogenesis in Focal Cortical Dysplasia23
Intravenous Thrombolysis with Tenecteplase for the Treatment of Acute Ischemic Stroke23
Inflammation in Cerebral Amyloid Angiopathy‐Related Transient Focal Neurological Episodes23
Annals of Neurology: Volume 92, Number 3, September 202222
Issue Information22
Association of Apolipoprotein E ɛ4 Allele with Enlarged Perivascular Spaces22
De Novo Missense Variants in SLC32A1 Cause a Developmental and Epileptic Encephalopathy Due to Impaired GABAergic Neurotransmission22
Disease Progression in Charcot–Marie–Tooth Disease Related to MPZ Mutations: A Longitudinal Study22
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Role of the Exposome in Neurodegenerative Disease: Recent Insights and Future Directions22
Re‐Emergence of Poliovirus in the United States: Considerations and Implications21
MuSK‐Myasthenia Gravis and Cancer21
MOG‐IgG‐Associated Bilateral Optic Neuritis in Temporal Relation to Monkeypox Vaccination21
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Microglial and Astrocytic Responses in the Human Midcingulate Cortex in Huntington's Disease21
Life‐Limiting Peripheral Organ Dysfunction in Feline Sandhoff Disease Emerges after Effective CNS Gene Therapy21
Cinematic Rendering of Twig‐Like Middle Cerebral Artery21
Longitudinal Alterations of Cerebral Blood Flow in High‐Contact Sports21
Fostering Academia‐Industry Partnerships to Facilitate Therapeutic Discoveries in Neurology: The Role of ANA as a Catalyst21
Enhancement of Glutamate Uptake as Novel Antiseizure Approach: Preclinical Proof of Concept21
Hydroxychloroquine for Primary Progressive Multiple Sclerosis20
Networks Underlie Temporal Onset of Dysplasia‐Related Epilepsy: A MELD Study20
Blood‐Based Proteomics for Adult‐Onset Focal Dystonias20
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Genetically Determined Low‐Density Lipoprotein Cholesterol and Risk of Subarachnoid Hemorrhage20
APOE Antibody Inhibits Aβ‐Associated Tau Seeding and Spreading in a Mouse Model20
Levodopa Impairs the Energy Metabolism of the Basal Ganglia In Vivo20
Pragmatic Clinical Trials in Neurology20
Ablating the Transporter Sodium‐Dependent Dicarboxylate Transporter 3 Prevents Leukodystrophy in Canavan Disease Mice20
Cognitive Effects of Deep Brain Stimulation in GBA‐Related Parkinson Disease20
Myelin Oligodendrocyte Glycoprotein Antibody‐Positive Patients Meeting the 2017 McDonald Criteria for Multiple Sclerosis: Challenges in Diagnosis and Treatment Decisions20
Reply to “Myelin Oligodendrocyte Glycoprotein Antibody‐Positive Patients Meeting the 2017 McDonald Criteria for Multiple Sclerosis: Challenges in Diagnosis and Treatment Decisions”20
Proteomic Indicators of Health Predict Alzheimer's Disease Biomarker Levels and Dementia Risk19
Dominant KPNA3 Mutations Cause Infantile‐Onset Hereditary Spastic Paraplegia19
Postictal Psychosis in Epilepsy: A Clinicogenetic Study19
Spasticity Predicts Motor Recovery for Patients with Subacute Motor Complete Spinal Cord Injury19
Divergent Causes and Convergent Mechanisms of SUDEP19
Intact HIV Proviruses Persist in the Brain Despite Viral Suppression with ART18
Mutations in HID1 Cause Syndromic Infantile Encephalopathy and Hypopituitarism18
Reply to “Type I IFN Signature in NOTCH1‐Related Leukoencephalopathy”18
Annals of Neurology: Volume 95, Number 3, March 202418
Cluster Headache Genomewide Association Study and Meta‐Analysis Identifies Eight Loci and Implicates Smoking as Causal Risk Factor18
Presynaptic Dopaminergic Imaging Characterizes Patients with REM Sleep Behavior Disorder Due to Synucleinopathy18
Annals of Neurology: Volume 93, Number 4, April 202318
Cerebrospinal Fluid Analysis Post–COVID‐19 Is Not Suggestive of Persistent Central Nervous System Infection18
Perimesencephalic Hemorrhage from A Superior Cerebellar Artery Dissection18
Annals of Neurology: Volume 90, Number 6, December 202118
AI in Neurology: Everything, Everywhere, All at Once Part 3: Surveillance, Synthesis, Simulation, and Systems18
Inhibition of Bone Morphogenetic Protein Signaling Prevents Tau Pathology in iPSC Derived Neurons and PS19 Mice18
The Starry Cortex of Aβ‐Related Angiitis18
Mutations in CLCN6 as a Novel Genetic Cause of Neuronal Ceroid Lipofuscinosis in Patients and a Murine Model18
Disparate Dementia Risk Factors Are Associated with Cognitive Impairment and Rates of Decline in African Americans18
Phase 1 Evaluation of Elezanumab (Anti–Repulsive Guidance Molecule A Monoclonal Antibody) in Healthy and Multiple Sclerosis Participants18
Neuroprotection of Low‐Frequency Repetitive Transcranial Magnetic Stimulation after Ischemic Stroke in Rats18
Reply to “Letter to the Editor, Regarding ‘Intravenous Thrombolysis in Patients Taking Direct Oral Anticoagulation Treatment Before Stroke Onset: Results from the Safe Implementations of Treatments in17
Association of Mismatch Profiles and Clinical Outcome from Endovascular Therapy in Large Infarct: A Post‐Hoc Analysis of the ANGELASPECT Trial17
Thalamic Influence on Slow Wave Slope Renormalization During Sleep17
Eligibility Rates among Racially and Ethnically Diverse US Participants in Phase 2 and Phase 3 Placebo‐Controlled, Double‐Blind, Randomized Trials of Lecanemab and Elenbecestat in Early Alz17
Issue Information17
Characterizing Frontal Lobe Seizure Semiology in Children17
Cost‐Effectiveness of Endovascular Thrombectomy in Patients with Large Ischemic Stroke17
Longitudinal Retinal Changes in MOGAD17
Natural History of Leigh Syndrome: A Study of Disease Burden and Progression17
Clinically Meaningful Magnetic Resonance Endpoints Sensitive to Preataxic Spinocerebellar Ataxia Types 1 and 317
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Amyloid‐Related Imaging Abnormalities in the DIAN‐TU‐001 Trial of Gantenerumab and Solanezumab: Lessons from a Trial in Dominantly Inherited Alzheimer Disease17
Obesity and Multiple Sclerosis Severity: A Mendelian Randomization Study17
Early Treatment with Vigabatrin Does Not Decrease Focal Seizures or Improve Cognition in Tuberous Sclerosis Complex: The PREVeNT Trial17
Divergent Associations of Slow‐Wave Sleep versus Rapid Eye Movement Sleep with Plasma Amyloid‐Beta17
Annals of Neurology: Volume 91, Number 2, February 202217
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Clinical Relevance of ‘Cap’ and ‘Track’ Development after Recent Small Subcortical Infarct16
Targeting Inflammasomes to Treat Neurological Diseases16
Annals of Neurology: Volume 96, Number 5, November 202416
Clonal Hematopoiesis and Acute Ischemic Stroke Outcomes16
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Ganaxolone versus Phenobarbital for Neonatal Seizure Management16
Cerebrovascular Function in Sporadic and Genetic Cerebral Small Vessel Disease16
Add‐On Deep Brain Stimulation versus Continued Vagus Nerve Stimulation for Childhood Epilepsy (ADVANCE): A Partially Randomized Patient Preference Trial15
In Vivo Assessment of Astrocyte Reactivity in Patients with Progressive Supranuclear Palsy15
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