Annals of Neurology

Papers
(The TQCC of Annals of Neurology is 13. The table below lists those papers that are above that threshold based on CrossRef citation counts [max. 250 papers]. The publications cover those that have been published in the past four years, i.e., from 2021-08-01 to 2025-08-01.)
ArticleCitations
Annals of Neurology: Volume 90, Number S27, October 2021183
Issue Information145
Efficacy and Safety of Ofatumumab Treatment for Anti‐NMDA Receptor Autoimmune Encephalitis (OFFAE): A Prospective, Multicenter Cohort Study133
Elevated Cerebrospinal Fluid Ubiquitin Carboxyl‐Terminal Hydrolase Isozyme L1 in Asymptomatic C9orf72 Hexanucleotide Repeat Expansion Carriers129
Issue Information110
Annals of Neurology: Volume 97, Number 1, January 2025103
Carotid Stent Fracture100
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Supratentorial Lymphocytic Inflammation with Parenchymal Perivascular Enhancement Responsive to Steroids: A Potentially Overlooked Diagnosis95
A Role for Insulin‐like Growth Factor 1 in the Generation of Epileptic Spasms in a murine model94
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Before, during, and after: An Argument for Safety and Improved Outcome of Thrombolysis in Acute Ischemic Stroke with Direct Oral Anticoagulant Treatment88
MS‐Driven Metabolic Alterations Are Recapitulated in iPSC‐Derived Astrocytes85
Vertebral Artery Pseudoaneurysm: Novel Marker of Bow Hunter's Syndrome81
Hypoparathyroidism Associated with Vascular Centrum Semiovale Calcifications80
Furthering Female Faculty: An American Neurological Association/Association of University Professors of Neurology Perspective79
HLA Associations of Intrathecal IgG Production against Specific Viruses in Multiple Sclerosis77
Interactions between High Seroreactivity to Human Herpes Virus 6A and Epstein–Barr Virus in MS Development: A Presymptomatic Case–Control Study75
A Letter Concerning a Role for Blood–Brain Barrier Dysfunction in Delirium following Noncardiac Surgery in Older Adults71
Cerebrospinal Fluid Flow in Patients with Huntington's Disease71
Cortical Microhemorrhage Presentation of Small Vessel Primary Angiitis of the Central Nervous System70
A Managed Care System with Telemedicine Support for Neurological Emergencies70
The Use of Antihypertensive Medication and In Vivo Alzheimer's Disease Pathology70
Staufen Impairs Autophagy in Neurodegeneration69
Dysregulation of Gut Microbiota‐Derived Neuromodulatory Amino Acid Metabolism in Human Immunodeficiency Virus‐Associated Neurocognitive Disorder: An Integrative Metagenomic and Metabolomic 67
Management of Cerebral Venous Thrombosis Due to Adenoviral COVID‐19 Vaccination66
Guanylate Kinase 1 Deficiency: A Novel and Potentially Treatable Mitochondrial DNA Depletion/Deletions Disease58
Plasma Metabolites Link Dietary Patterns to Stroke Risk57
Effect of Imaging Markers on Reperfusion Therapy in Basilar Artery Occlusion57
Severity of GNAO1‐Related Disorder Correlates with Changes in G‐Protein Function57
Blood Pressure after Successful Endovascular Therapy: A Systematic Review and Meta‐Analysis of Randomized Control Trials56
Network Localization of Awareness in Visual and Motor Anosognosia55
Probabilistic Mapping Reveals Optimal Stimulation Site in Essential Tremor54
Association of Retromer Deficiency and Tau Pathology in Down Syndrome52
Diet, Pace of Biological Aging, and Risk of Dementia in the Framingham Heart Study51
Prevalence of Cerebral Amyloid Angiopathy and Associated Risk of Subsequent Ischemic and Hemorrhagic Stroke and Mortality in a Nationwide Cohort50
Epidemiology, Survival, and Clinical Characteristics of Inclusion Body Myositis49
Suvorexant Acutely Decreases Tau Phosphorylation and Aβ in the Human CNS49
Biological Age Acceleration and Motoric Cognitive Risk Syndrome49
Annals of Neurology: Volume 94, Number S30, September 202348
Issue Information48
Annals of Neurology: Volume 90, Number S26, September 202148
Micro‐Doses of DNP Preserve Motor and Muscle Function with a Period of Functional Recovery in Amyotrophic Lateral Sclerosis Mice48
Septin‐5 and ‐7‐IgGs: Neurologic, Serologic, and Pathophysiologic Characteristics48
Cover Image48
Illusions of Self‐Motion during Magnetic Resonance‐Guided Focused Ultrasound Thalamotomy for Tremor48
Sports Concussion and Category Mistakes46
Reply to “Core Penumbral Mismatch: An Independent Predictor of Stroke Poorer Outcome”45
MEK Pathway Inhibitor‐Mediated Response in BRAF V600‐Mutant Melanoma with Brain Parenchymal and Leptomeningeal Metastases45
RAN Translation of C9orf72‐Related Dipeptide Repeat Proteins in Zebrafish Recapitulates Hallmarks of Amyotrophic Lateral Sclerosis and Identifies Hypothermia as a Therapeutic Strategy43
APOE2 Exacerbates TDP‐43 Related Toxicity in the Absence of Alzheimer Pathology42
Improving Early Recognition of Treatment‐Responsive Causes of Rapidly Progressive Dementia: The STAM3P Score42
Regional Brain Metabolism across the Alzheimer's Disease Continuum in Down Syndrome41
Longitudinal Imaging Biomarkers Correlate with Progressive Motor Deficit in the Mouse Model of Charlevoix‐Saguenay Ataxia41
Dopamine Transporter Imaging as Objective Monitoring Biomarker in Parkinson's Disease40
Development of Parkinson Disease and Its Relationship with Incidentally Discovered White Matter Disease and Covert Brain Infarction in a Real‐World Cohort40
Correction: GATA1‐Mediated Transcriptional Regulation of the γ‐Secretase Activating Protein Increases Aβ Formation in Down Syndrome40
GABRA1‐Related Disorders: From Genetic to Functional Pathways40
Correction: Regional Glymphatic Abnormality in Behavioral Variant Frontotemporal Dementia40
A Combined Panel of Salivary Biomarkers in de novo Parkinson's Disease39
Subicular Caspase‐1 Contributes to Pharmacoresistance in Temporal Lobe Epilepsy39
Intravenous Thrombolysis in Patients Taking Direct Oral Anticoagulation Treatment Before Stroke Onset: Results from the Safe Implementations of Treatments in Stroke International Stroke Registry38
Visual Features in Stereo‐Electroencephalography to Predict Surgical Outcome: A Multicenter Study38
GGC Repeat Expansion of RILPL1 is Associated with Oculopharyngodistal Myopathy37
Association of Seizure Control with Mortality, Cognition, and Function in People With Dementia37
Choroid Plexus Enlargement Exacerbates White Matter Hyperintensity Growth through Glymphatic Impairment37
Ultrastructural Axon–Myelin Unit Alterations in Multiple Sclerosis Correlate with Inflammation37
Trials for Slowly Progressive Neurogenetic Diseases Need Surrogate Endpoints37
Tenascin‐R Autoimmunity: Isolated Tremor Reversed with Immunotherapy36
NINDS Corner: The Helping to End Addiction Long‐Term Initiative and Pain Neurology36
Annals of Neurology: Volume 90, Number 3, September 202136
Reply to “Clinical Relevance of Genetic Variants in Juvenile Stroke Patients: A Plea for a Precise Classification”36
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Bilateral Hearing Loss Caused by Inferior Collicular Infarction35
Reply to “Letter on Multiple Acyl‐Coenzyme A Dehydrogenase Deficiency Is Associated with Sertraline Use”35
Typical Radiological Features of a Rare Lateral Ventricular Liponeurocytoma35
Brain Iron Dysregulation in Iron Deficiency Anemia‐Related Restless Leg Syndrome Revealed by Neuron‐Derived Extracellular Vesicles: A Case–Control Study35
Is there an Association between Tuber Involvement of the Fusiform Face Area in Autism Diagnosis?34
Bleeding Risk of Dual Antiplatelet Therapy after Minor Stroke or Transient Ischemic Attack34
Reply to “Is There an Association between Tuber Involvement of the Fusiform Face Area in Autism Diagnosis?”34
Promise of Nucleic Acid Therapeutics for Amyotrophic Lateral Sclerosis34
Nocturnal Pulse Event Frequency Is Reduced in Multiple System Atrophy34
Reply to “Chance Bias Arising from TSC2 Mutation Imbalance in the PREVeNT Trial”34
Seizures after Ischemic Stroke: A Matched Multicenter Study33
Autoimmune Glial Fibrillary Acidic Protein Astrocytopathy Is Associated with HLA‐A*3303 and HLA‐DPB1*050133
High‐Dose Pulse Glucocorticoid Treatment Prevents White Matter Spinal Cord Pseudoatrophy in Newly Diagnosed Multiple Sclerosis33
Neuroimaging Biomarkers for Friedreich Ataxia: A Cross‐Sectional Analysis of the TRACKFA Study33
Issue Information32
Fighting Amyotrophic Lateral Sclerosis by Protecting the Liver? A Prospective Cohort Study32
Signs of Cortical Inflammation in Migraine Measured with Quantitative Magnetic Resonance Imaging: A Registry for Migraine (REFORM) Study32
Issue Information32
Recessive Variants in PIGG Cause a Motor Neuropathy with Variable Conduction Block, Childhood Tremor, and Febrile Seizures: Expanding the Phenotype32
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Uncovering Image‐Driven Subtypes with Distinct Pathology and Clinical Course in Autopsy‐Confirmed Four Repeat Tauopathies32
Trigeminal Trophic Syndrome from Lateral Medullary Stroke32
Prophylactic Fetal Creatine Supplementation Improves Post‐Asphyxial EEG Recovery and Reduces Seizures in Fetal Sheep: Implications for Hypoxic–Ischemic Encephalopathy32
Histopathological Correlates of Lobar Microbleeds in False‐Positive Cerebral Amyloid Angiopathy Cases31
Greater Diffusion Restriction in White Matter in Preclinical Alzheimer Disease31
Automated Neuroprognostication Via Machine Learning in Neonates with Hypoxic‐Ischemic Encephalopathy31
Actigraphy Enables Home Screening of Rapid Eye Movement Behavior Disorder in Parkinson's Disease31
Genome‐Wide Analysis of Structural Variants in Parkinson Disease31
Compensated Hypogonadism Identified in Males with Cluster Headache: A Prospective Case‐Controlled Study31
In Memoriam: Arthur Knight Asbury, MD (1928–2022)30
Responsiveness of the Scale for the Assessment and Rating of Ataxia and Natural History in 884 Recessive and Early Onset Ataxia Patients30
Issue Information – TOC30
Issue Information30
Stage‐Dependent Biomarker Changes in Spinocerebellar Ataxia Type 330
COVID‐19‐Associated Critical Illness Myopathy with Direct Viral Effects30
Issue Information30
Determinants of Infarct Core Growth During Inter‐hospital Transfer for Thrombectomy30
Correction: Decreased Cerebrospinal Fluid Amyloid β 38, 40, 42, and 43 Levels in Sporadic and Hereditary Cerebral Amyloid Angiopathy30
ANA Investigates: Atrial Fibrillation after Stroke30
Spoken Language Alterations can Predict Phenoconversion in Isolated Rapid Eye Movement Sleep Behavior Disorder: A Multicenter Study29
Pivotal Role of Slitrk1 in Adult Striatal Cholinergic Neurons in Mice: Implication in Tourette Syndrome29
SRPK3 Is Essential for Cognitive and Ocular Development in Humans and Zebrafish, Explaining X‐Linked Intellectual Disability29
Cortical Correlates of Gait Compensation Strategies in Parkinson Disease29
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Evaluation of Soluble Colony Stimulating Factor 1 Receptor (CSF1R) in Peripheral Blood as a Diagnostic Marker of CSF1R‐Related Disorder (CSF1RRD) in a Muri28
ANA Podcasts & Webinars: Genetics of Epilepsy28
Effect of Cumulative Exposure to Ocrelizumab on Memory B‐Cell Repopulation Dynamics in Multiple Sclerosis28
Disease‐Modifying Drugs Extend Survival in Hereditary Transthyretin Amyloid Polyneuropathy28
Adolescent Headache Due to Congenital Pelvic/Sacral Vascular Malformation28
Cerebral Small Vessel Disease Progression Increases Risk of Incident Parkinsonism28
Reply to “VAERS Could Miss or Misinterpret Neurological Side Effects of COVID Vaccinations”28
Extra Movements in Healthy People: Challenging the Definition and Diagnostic Practice of Tic Disorders28
Search Strategies for Alzheimer Protector Genes28
CADASIL Affects Multiple Aspects of Cerebral Small Vessel Function on 7T‐MRI28
Ultra‐Low Level Somatic Mutations and Structural Variations in Focal Cortical Dysplasia Type II27
Comparative Safety of Antiseizure Medication Monotherapy for Major Malformations27
Subcortical Volumes as Early Predictors of Fatigue in Multiple Sclerosis27
Risk of Multiple Sclerosis in People Living with HIV: An International Cohort Study27
Application of the Amyloid/Tau/Neurodegeneration Framework in Cognitively Intact Adults: The CABLE Study27
Annals of Neurology: Volume 95, Number 4, April 202427
Smouldering‐Associated Worsening in Multiple Sclerosis: An International Consensus Statement on Definition, Biology, Clinical Implications, and Future Directions27
Annals of Neurology: Volume 96, Number 2, August 202426
Issue Information26
NORSE, FIRES, and a Polygenic Trickle of Autoimmunity26
Issue Information26
Correction to Lyden P, Pryor KE, Coffey CS, et al. Final results of the RHAPSODY trial: a multi‐center, phase 2 trial using a continual reassessment method to determine the safety and toler26
Issue Information26
Systemic Metabolic Alteration Dependent on the Thyroid‐Liver Axis in Early PD25
Inflammation in Cerebral Amyloid Angiopathy‐Related Transient Focal Neurological Episodes25
Limbic Stimulation Drives Mania in STN‐DBS in Parkinson Disease: A Prospective Study25
Annual Report from the Editor‐in‐Chief (2024)25
High Levels of Perivascular Inflammation and Active Demyelinating Lesions at Time of Death Associated with Rapidly Progressive Multiple Sclerosis Disease Course: A Retrospective Postmortem Cohort Stud25
Activated Wake Systems in Narcolepsy Type 125
Disease Progression in Charcot–Marie–Tooth Disease Related to MPZ Mutations: A Longitudinal Study25
Role of the Exposome in Neurodegenerative Disease: Recent Insights and Future Directions25
Disease Characteristics and Treatments Associated with Outcome in Primary Angiitis of the Central Nervous System—A Multicenter Cohort Study in 163 Patients25
“Don't Throw the Baby out with the Bathwater”25
Neutrophils Are Associated with Higher Risk of Incident Amyotrophic Lateral Sclerosis in a BMI‐ and Age‐Dependent Manner24
Emerging Management Challenges Posed by Atrial Fibrillation Detected After Stroke24
A Carotid Web with Atherosclerotic Plaque24
Insular Stimulation Produces Mental Clarity and Bliss24
Brainstem Ischemic Syndrome in NF2‐Related Schwannomatosis24
Sex Differences in Trends in Stroke Recurrence and Postrecurrence Mortality 2000–2020: Population‐Based Brain Attack Surveillance in Corpus Christi Project24
Social Health and Cognitive Change in Old Age: Role of Brain Reserve24
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Cinematic Rendering of Extracranial to Intracranial Arterial Bypass24
Vessel Wall Imaging of a Carotid Web24
Internal Carotid Artery Pseudoaneurysm and Unilateral Vocal Cord Paralysis Secondary to Parapharyngeal Space Abscess24
Network Localization of Pediatric Lesion‐Induced Dystonia24
Intravenous Thrombolysis with Tenecteplase for the Treatment of Acute Ischemic Stroke23
Temporal Pattern of Cortical Hypoxia in Multiple Sclerosis and Its Significance on Neuropsychological and Clinical Measures of Disability23
De Novo Missense Variants in SLC32A1 Cause a Developmental and Epileptic Encephalopathy Due to Impaired GABAergic Neurotransmission23
Association of Apolipoprotein E ɛ4 Allele with Enlarged Perivascular Spaces23
Diagnosing Epilepsy with Normal Interictal EEG Using Dynamic Network Models23
Charcot Joint23
Fixating with the Paretic Eye: Evidence of “Fixation Duress” on PET Imaging23
Salivary CGRP and Erenumab Treatment Response: Towards Precision Medicine in Migraine23
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Enhancement of Glutamate Uptake as Novel Antiseizure Approach: Preclinical Proof of Concept22
Prediction of Cognitive Heterogeneity in Parkinson's Disease: A 4‐Year Longitudinal Study Using Clinical, Neuroimaging, Biological and Electrophysiological Biomarkers22
Cinematic Rendering of Twig‐Like Middle Cerebral Artery22
Issue Information22
Annals of Neurology: Volume 92, Number 3, September 202222
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Ablating the Transporter Sodium‐Dependent Dicarboxylate Transporter 3 Prevents Leukodystrophy in Canavan Disease Mice21
Life‐Limiting Peripheral Organ Dysfunction in Feline Sandhoff Disease Emerges after Effective CNS Gene Therapy21
MuSK‐Myasthenia Gravis and Cancer21
MOG‐IgG‐Associated Bilateral Optic Neuritis in Temporal Relation to Monkeypox Vaccination21
Fostering Academia‐Industry Partnerships to Facilitate Therapeutic Discoveries in Neurology: The Role of ANA as a Catalyst21
Networks Underlie Temporal Onset of Dysplasia‐Related Epilepsy: A MELD Study20
Cognitive Effects of Deep Brain Stimulation in GBA‐Related Parkinson Disease20
Divergent Causes and Convergent Mechanisms of SUDEP20
Myelin Oligodendrocyte Glycoprotein Antibody‐Positive Patients Meeting the 2017 McDonald Criteria for Multiple Sclerosis: Challenges in Diagnosis and Treatment Decisions20
Reply to “Myelin Oligodendrocyte Glycoprotein Antibody‐Positive Patients Meeting the 2017 McDonald Criteria for Multiple Sclerosis: Challenges in Diagnosis and Treatment Decisions”20
APOE Antibody Inhibits Aβ‐Associated Tau Seeding and Spreading in a Mouse Model20
Blood‐Based Proteomics for Adult‐Onset Focal Dystonias20
Spasticity Predicts Motor Recovery for Patients with Subacute Motor Complete Spinal Cord Injury20
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Pragmatic Clinical Trials in Neurology20
Cluster Headache Genomewide Association Study and Meta‐Analysis Identifies Eight Loci and Implicates Smoking as Causal Risk Factor20
Proteomic Indicators of Health Predict Alzheimer's Disease Biomarker Levels and Dementia Risk20
Presynaptic Dopaminergic Imaging Characterizes Patients with REM Sleep Behavior Disorder Due to Synucleinopathy19
Microglial and Astrocytic Responses in the Human Midcingulate Cortex in Huntington's Disease19
Postictal Psychosis in Epilepsy: A Clinicogenetic Study19
Decoding the Clinical Features that Associate with Progression, Causes, and Outcomes in Patients with Suspected Rapidly Progressive Dementia19
Intact HIV Proviruses Persist in the Brain Despite Viral Suppression with ART19
Genetically Determined Low‐Density Lipoprotein Cholesterol and Risk of Subarachnoid Hemorrhage19
Timing of Changes in Alzheimer's Disease Plasma Biomarkers as Assessed by Amyloid and Tau PET Clocks19
Neuroprotection of Low‐Frequency Repetitive Transcranial Magnetic Stimulation after Ischemic Stroke in Rats19
Levodopa Impairs the Energy Metabolism of the Basal Ganglia In Vivo19
Longitudinal Alterations of Cerebral Blood Flow in High‐Contact Sports19
AI in Neurology: Everything, Everywhere, All at Once Part 3: Surveillance, Synthesis, Simulation, and Systems19
Autosomal Recessive Cerebellar Ataxias: Translating Genes to Therapies19
The Starry Cortex of Aβ‐Related Angiitis18
Hydroxychloroquine for Primary Progressive Multiple Sclerosis18
Annals of Neurology: Volume 90, Number 6, December 202118
Reply to “Type I IFN Signature in NOTCH1‐Related Leukoencephalopathy”18
Cost‐Effectiveness of Endovascular Thrombectomy in Patients with Large Ischemic Stroke18
Reply to “Letter to the Editor, Regarding ‘Intravenous Thrombolysis in Patients Taking Direct Oral Anticoagulation Treatment Before Stroke Onset: Results from the Safe Implementations of Treatments in18
Re‐Emergence of Poliovirus in the United States: Considerations and Implications18
Annals of Neurology: Volume 93, Number 4, April 202318
Phase 1 Evaluation of Elezanumab (Anti–Repulsive Guidance Molecule A Monoclonal Antibody) in Healthy and Multiple Sclerosis Participants18
Obesity and Multiple Sclerosis Severity: A Mendelian Randomization Study18
Perimesencephalic Hemorrhage from A Superior Cerebellar Artery Dissection18
Dominant KPNA3 Mutations Cause Infantile‐Onset Hereditary Spastic Paraplegia18
Annals of Neurology: Volume 95, Number 3, March 202418
Thalamic Influence on Slow Wave Slope Renormalization During Sleep18
Association of Mismatch Profiles and Clinical Outcome from Endovascular Therapy in Large Infarct: A Post‐Hoc Analysis of the ANGELASPECT Trial17
Cerebrospinal Fluid Analysis Post–COVID‐19 Is Not Suggestive of Persistent Central Nervous System Infection17
Characterizing Frontal Lobe Seizure Semiology in Children17
Eligibility Rates among Racially and Ethnically Diverse US Participants in Phase 2 and Phase 3 Placebo‐Controlled, Double‐Blind, Randomized Trials of Lecanemab and Elenbecestat in Early Alz17
Divergent Associations of Slow‐Wave Sleep versus Rapid Eye Movement Sleep with Plasma Amyloid‐Beta17
Amyloid‐Related Imaging Abnormalities in the DIAN‐TU‐001 Trial of Gantenerumab and Solanezumab: Lessons from a Trial in Dominantly Inherited Alzheimer Disease17
Disparate Dementia Risk Factors Are Associated with Cognitive Impairment and Rates of Decline in African Americans17
Longitudinal Retinal Changes in MOGAD17
Clinically Meaningful Magnetic Resonance Endpoints Sensitive to Preataxic Spinocerebellar Ataxia Types 1 and 317
Inhibition of Bone Morphogenetic Protein Signaling Prevents Tau Pathology in iPSC Derived Neurons and PS19 Mice17
Mutations in CLCN6 as a Novel Genetic Cause of Neuronal Ceroid Lipofuscinosis in Patients and a Murine Model17
Early Treatment with Vigabatrin Does Not Decrease Focal Seizures or Improve Cognition in Tuberous Sclerosis Complex: The PREVeNT Trial17
Natural History of Leigh Syndrome: A Study of Disease Burden and Progression17
Clinical Relevance of ‘Cap’ and ‘Track’ Development after Recent Small Subcortical Infarct16
CRISPR‐Based KCC2 Upregulation Attenuates Drug‐Resistant Seizure in Mouse Models of Epilepsy16
Independent Confirmation16
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The Differing Effects of Sleep on Ictal and Interictal Network Dynamics in Drug‐Resistant Epilepsy16
Letter on Wine Glass Sign in Bulbar‐Onset Amyotrophic Lateral Sclerosis16
Cerebrovascular Function in Sporadic and Genetic Cerebral Small Vessel Disease16
Annals of Neurology: Volume 91, Number 2, February 202216
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Annals of Neurology: Volume 96, Number 5, November 202416
Mapping Molecular Pathways of Multiple Sclerosis: A Gene Prioritization and Network Analysis of White Matter Pathology Transcriptomics16
Frequency and Early Predictors of Cognitive Deterioration in Amyotrophic Lateral Sclerosis: A Longitudinal Population‐Based Study16
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