Journal of Cystic Fibrosis

Papers
(The TQCC of Journal of Cystic Fibrosis is 0. The table below lists those papers that are above that threshold based on CrossRef citation counts [max. 250 papers]. The publications cover those that have been published in the past four years, i.e., from 2021-06-01 to 2025-06-01.)
ArticleCitations
EPS10.06 Highly-effective CFTR modulation is associated with greater height and peak lung function in children with cystic fibrosis233
EPS8.02 Evolving physiotherapy airway clearance technique (ACT) interventions during cystic fibrosis (CF) pregnancy in the variant specific therapy (VST) era117
P172 Oscillometry: assessment of bronchial obstruction in children with cystic fibrosis87
P078 Hyperacute response to cystic fibrosis transmembrane conductance regulator modulation80
P402 Separation anxiety or a Kaftrio side effect? Implementation of cognitive behavioural therapy strategies with a young child with cystic fibrosis (CF): A clinical case study79
P408 The halo effect in cystic fibrosis: when educated patients in turn educate their family carers78
EPS10.07 Exacerbation characteristics and clinical outcomes in the elexacaftor/tezacaftor/ivacaftor era: same-same but different?74
WS08.03 How does elexacaftor/tezacaftor/ivacaftor affect improvement in exercise capacity and body composition in adults with cystic fibrosis who have completed an exercise intervention?73
P131 Effect of deprescribing from inhaled corticosteroids in people with cystic fibrosis: challenges & opportunities for a target trial emulation using the UK CF Registry68
WS15.05 Improvements in structural lung disease in people with CF aged 12 and above on elexacaftor/tezacaftor/ivacaftor are sustained for up to two years67
P109 Safety of elexacaftor/tezacaftor/ivacaftor in patients 6 through 18 years with cystic fibrosis and at least one F508del allele: a retrospective Italian multicenter study63
P296 Characteristics of carbohydrate metabolism disorders in children with cystic fibrosis in the Moscow region63
WS13.03 Anti-inflammatory effects of elexacaftor/tezacaftor/ivacaftor in adults with cystic fibrosis heterozygous for F508del62
39 Using mouse models to understand the critical roles of granulocyte macrophage colony stimulating factor and macrophages for control of pulmonary Mycobacterium abscessus infection62
304 Assessing a novel dual-endonuclease system in restoring CFTR expression in cystic fibrosis humanized mouse and human airway models56
320 Gain-of-function CFTR mutation improves function of W1282X CFTR56
184 Bioengineered three-dimensional cystic fibrosis lung airway model for drug testing55
490 What are the experiences of cystic fibrosis clinical nurse specialists? Are systemic practice ideas unknowingly incorporated when working with children and families?53
526 Non-surgical management of urinary incontinence in women with cystic fibrosis46
586 Description of a novel therapeutic support group for siblings of children with cystic fibrosis: Siblings Supporting Others and Achieving Resilience45
808 Implementation of physical therapy and exercise education in annual cystic fibrosis clinic45
99 Development and validation of a deep neural network to predict antimicrobial resistance in people with cystic fibrosis using routinely collected electronic healthcare record data45
773 A quality improvement project to improve the evaluation of low bone density in people with cystic fibrosis44
209 Inositol-requiring enzyme 1β is a therapeutic target for cystic fibrosis airway muco-obstructive disease44
463: Clearance of colonized bacterial species in CF patients before and after elexacaftor/tezacaftor/ivacaftor43
410 Multidisciplinary collaboration for transition readiness and planning42
460: Prevalence of antimicrobial resistance mutations in Mycobacterium abscessus and associations with in vitro susceptibility testing41
465: Intestinal function and transit relates to microbial dysbiosis in the CF gut40
568: Quantifying regional pulmonary ventilation changes pre-/postivacaftor treatment in same subject using hyperpolarized 3He MRI38
491 The Cystic Fibrosis Questionnaire–Revised and body image in adults in the era of elexacaftor-tezacaftor-ivacaftor38
585: Development of a novel, cell-free, in vitro, high-throughput screening system for readthrough agents of nonsense mutations36
620: Iterative screen identifies amphiphilic peptides that confer enhanced delivery of CRISPR-associated nucleases and adenine base editors to airway epithelia35
524 Acid suppression therapy and associations with growth, gut microbiome, and early-onset lung disease in young children with cystic fibrosis35
462 Cystic fibrosis mental health and wellness questionnaire—factors and properties34
488: Bile acids, bacterial colonization, and lung inflammatory markers in infants with cystic fibrosis34
P221 Tension-free vaginal tape – a 15-year review of effect on urinary incontinence in patients with cystic fibrosis34
508: Extracellular vesicles mediate bacteria–immune cell interactions in the respiratory tract34
P209 Physical fitness and habitual physical activity in children with cystic fibrosis - do they improve with elexacaftor/tezacaftor/ivacaftor therapy?34
353: Electrolyte transport properties assay revealed less carbachol-stimulated short-circuit current in cultured human small airway epithelia33
372 Cystic fibrosis does exist in India! A successful approach to education and improving awareness of cystic fibrosis of physicians and caregivers in India33
670: F508del and G542X sheep models exhibit a severe cystic fibrosis phenotype, and their tracheal epithelial cells respond to human therapeutics in vitro32
558 Development of a gene editing strategy to treat cystic fibrosisassociated liver disease32
140: Oh gee! Time tested OGTT annual screening improvement: A single-center experience32
P029 Antisense oligonucleotide-based drug development for cystic fibrosis patients carrying the 2789+5 G-to-A splicing mutation31
249 Pharmacological rescue of CFTR premature termination codon mutations by novel small molecules31
148: Sustainably implementing impactful pre-visit planning using the electronic health record31
P052 Introduction of an innovative “pill-swallowing school” in a cystic fibrosis paediatric population within a tertiary centre31
43 Bacteriophages that kill Pseudomonas aeruginosa induce heterogenous cellular responses in the airway epithelium30
11 Examining antibiotic regimen spectrum and clinical outcomes of pulmonary exacerbation treatment30
100 Vancomycin demonstrates activity against Mycobacterium abscessus in combination with guideline-recommended antibiotics under physiologically relevant stress conditions30
54 Recombinant pyocins as emerging therapies against respiratory infections with Pseudomonas aeruginosa30
13 Extended-interval dosing of amikacin against Mycobacterium abscessus reduces efficacy in vitro30
647 Impact of newborn screening program with NextGen sequencing on direct patient care29
624 Evaluating precision medicine tools in cystic fibrosis for racial and ethnic fairness29
WS11.04 Confirmatory genetic testing for all cystic fibrosis screen positive newborns: a 12-year analysis28
WS11.03 Repeated sweat testing in children with cystic fibrosis transmembrane conductance regulator-related metabolic syndrome/cystic fibrosis screen positive, inconclusive diagnosis (CRMS/CFSPID)28
ePS2.02 Comparison of FEV on a remote spirometry device with hospital software in an adult cystic fibrosis cohort28
WS10.03 Impact of triple CFTR modulator therapy on urinary incontinence symptoms in adults with cystic fibrosis28
P083 Decreased respiratory burst in circulating neutrophils after initiation of CFTR modulator therapy in cystic fibrosis patients with chronic lung infections27
ePS4.03 Outcomes of COVID-19 in patients with cystic fibrosis in Wales, UK27
ePS3.05 Induced levofloxacin resistance persists in evolved lineages of Pseudomonas aeruginosa isolates from people with cystic fibrosis after exposure to other inhaled antibiotics27
P106 Upper airway disease in adults with cystic fibrosis: a cross-sectional study26
288 CFTR genetic variants and association with cancer26
220: Using lean methodologies to influence oral glucose tolerance test completion in cystic fibrosis patients26
314 A role for CFTR in pancreatitis25
292 Mechanism of CFTR modulation on endothelial mechanosensitive channels25
P143 Bronchopulmonary infection/colonisation in Spanish cystic fibrosis patients: preliminary results of a multicentre study25
5: Testosterone deficiency in men with cystic fibrosis: Understanding prevalence & association with clinical outcomes25
314: The COVID-19 pandemic and trends in anxiety and depressive symptoms in adolescents with cystic fibrosis and their caregivers24
329 Intrinsic conformational dynamics required for CFTR gating cycle revealed by single-molecule Förster resonance energy transfer24
WS03.03 Qualitative analyses of the experiences of people with end-stage cystic fibrosis lung disease receiving ELX/TEZ/IVA24
306: Behavioral health resources and screening in military cystic fibrosis centers: A survey24
348 Single-cell multi-omics profiling reveals novel regulatory networks of CFTR in the kidney24
Theranostics vs theratyping or theranostics plus theratyping?23
419 Role of macrophage cystic fibrosis transmembrane conductance regulator in lung inflammation22
447 Mucociliary interactions and the vertical clearance assay 2.022
341 Improving care for pregnant people with cystic fibrosis by increasing knowledge of obstetric providers22
487 Evaluating use of doxycycline versus vancomycin for treatment of methicillin-resistant Staphylococcus aureus–associated acute pulmonary exacerbations in people with cystic fibrosis22
633 Extracellular vesicles as delivery vectors to enhance killing of bacteria and viruses by airway-recruited human neutrophils22
59 Improving mycobacterial sputum culture collection in adult patients during the highly effective modulator therapy era21
132 Respiratory symptom changes during menstrual cycles in women with cystic fibrosis21
257 Rapid health decline in young cystic fibrosis transmembrane conductance regulatorG551D ferrets after discontinuation of cystic fibrosis transmembrane conductance regulator modulator21
P227 Life threatening infection with a highly resistant Achromobacter xylosoxidans strain20
P478 Multiple breath inert gas wash out in infants and toddlers with cystic fibrosis before and after initiating inhaled hypertonic saline20
291 Development and validation of the Cystic Fibrosis Stress Questionnaire: A cystic fibrosis–specific measure of perceived stress20
Sexual and reproductive health experiences and care of adult women with cystic fibrosis20
145 Prescription of elexacaftor/tezacaftor/ ivacaftor in lung transplant recipients with cystic fibrosis20
417 Resolvin D1 reduces cystic fibrosis lung disease and inflammation associated with mucus obstruction20
P024 Analysis of the effect of cytochrome P450 genes polymorphism on the efficacy and safety of CFTR modulator therapy in cystic fibrosis20
260 Cystic fibrosis transmembrane conductance regulator modulator–associated liver inflammation in pediatric cystic fibrosis20
644 Timely initiation of pancreatic enzyme replacement therapy for surgical cystic fibrosis infants in the neonatal intensive care unit19
Immune response of polarized cystic fibrosis airway epithelial cells infected with Influenza A virus19
529 Are adults with cystic fibrosis choosing to continue with airway clearance therapy in the era of highly effective gene modulator therapy?19
260 RCT2100 rescue of cystic fibrosis (CF) transmembrane conductance regulator function in CF human bronchial epithelial cells and mucociliary clearance in CF ferrets19
365 Differential effects of (S)- and (R)-vanzacaftor on BKCa potentiation and CFTR correction18
235 Differential regulation of immune function by highly effective CFTR modulators in THP-1-derived macrophages18
Impact of azithromycin on serum inflammatory markers in children with cystic fibrosis and new Pseudomonas18
27 Standing up to the “bully”: Staphylococcus aureus can sustain long-term infection in the presence of Pseudomonas aeruginosa and may outcompete in the cystic fibrosis airway18
564 “How do you live the best life you can with this pain?” A qualitative study of the challenges of living with CF and pain in the modulator era18
51 Outcomes after SARS-CoV-2 infection in Canadians with cystic fibrosis: Analyses using the Canadian Cystic Fibrosis Registry18
332 Vocational rehabilitation services for people with cystic fibrosis: Predictors of employment outcomes18
480 Weight stigma among healthcare professionals treating CF in North America18
679 Effect of hybrid closed loop insulin delivery on glycemic control in adolescents and adults with cystic fibrosis-related diabetes18
Characteristics associated with cystic fibrosis-related pulmonary exacerbation treatment location18
Serological biomarkers for the diagnosis of Mycobacterium abscessus infections in cystic fibrosis patients18
558 Challenges faced by parents of children with cystic fibrosis in Ireland: The Irish Comparative Outcome Study of Cystic Fibrosis18
Treatment of intestinal and liver features in cystic fibrosis mice by the osmotic laxative polyethylene glycol17
Improved early growth in Danish children with cystic fibrosis from 2000-202217
Using heart rate data from wrist worn activity trackers to define thresholds for moderate to vigorous physical activity in children and young people with cystic fibrosis17
“Mind the gap”- will we ever see equal median predicted survival for males and females in cystic fibrosis?17
Neurovascular complications post bronchial artery embolisation in patients with cystic fibrosis. A 7-year single centre retrospective review17
Decline in HbA1c during the first year of elexacaftor/tezacaftor/ivacaftor treatment in the Danish cystic fibrosis cohort17
Evidence for secondary ciliary dyskinesia in patients with cystic fibrosis17
Autoimmunity in people with cystic fibrosis17
Clinical efficacy of CFTR modulator therapy in people with cystic fibrosis carrying the I1234V mutation16
Restoring airway epithelial homeostasis in Cystic Fibrosis16
Preclinical atherosclerosis in cystic fibrosis: Two distinct presentations are related to pancreatic status16
European survey of newborn bloodspot screening for CF: opportunity to address challenges and improve performance16
Risk factors for cystic fibrosis arthropathy: Data from the German cystic fibrosis registry16
Structure basis of CFTR folding, function and pharmacology16
When CFSPID becomes CF15
P243 The effect of hypoxic conditions on Burkholderia cenocepacia clinical isolates from individuals with cystic fibrosis15
P418 Patient satisfaction and clinical effectiveness of using the I-neb in children with cystic fibrosis (CF) in Wales15
EPS5.08 Elexacaftor/tezacaftor/ ivacaftor reduces need for pancreatic enzymes, enteral feeding and omeprazole use without causing excessive weight gain: a 2-year observational study15
P007 Experience of using intestinal current measurement (ICM) in Russia15
P282 Implementing routine assessment of gastrointestinal outcome measures in the cystic fibrosis clinic15
P360 Mental health in cystic fibrosis patients: predictive factors and psychopathology15
Vitamin D supplementation in patients with cystic fibrosis: A systematic review and meta-analysis15
P134 Evaluation of multidisciplinary ambulatory care cost among children with cystic fibrosis: a comparative study between cystic fibrosis centers in Ireland and the United States15
P169 Vitamin absorption after the introduction of elexacaftor/tezacaftor/ivacaftor in children and adolescents diagnosed with cystic fibrosis15
P295 The results of colorectal cancer screening in patients with cystic fibrosis in Wales15
P382 Cystic fibrosis and disordered eating behaviour: a collaborative approach to improve care15
WS13.01 The cystic fibrosis Home Sputum-Induction Trial (CF-HomeSpIT - ISRCTN86523335) to evaluate home sputum-induction and early morning saliva sampling in children with cystic fibrosis15
P104 The dynamics of health of children with cystic fibrosis in Russian Federation according to the registry data during last 10 years15
P387 Reviews and outcomes from a new pregnancy support service at a large cystic fibrosis centre15
Personalized therapy with CFTR modulators: Response of p.Ile148Asn variant14
P219 Otorhinolaryngologic, audiological and genetic findings in children with cystic fibrosis: a tertiary care experience14
166 Single-cell and bulk transcriptomes in the nasal epithelium of people with cystic fibrosis demonstrate cell-type compositional heterogeneity14
142 Elexacaftor-tezacaftor-ivacaftor and spirometry-controlled chest CT scores in children with cystic fibrosis aged 6 to 1114
84 Plasmids acquired during the course of cystic fibrosis infections cause extreme antibiotic resistance in Pseudomonas aeruginosa14
WS06.03 A real-world evaluation of remote monitoring in cystic fibrosis care: a mixed-methods multicentre observational study14
P017 The role of the VDR gene in the formation of clinical manifestations and complications in cystic fibrosis14
536 Effect of elexacaftor-tezacaftor-ivacaftor on nutritional status and glucose metabolism in children and adolescents with cystic fibrosis14
72 Investigating polymicrobial interactions involving Streptococcus in the cystic fibrosis airway14
634: Identification of binding sites for ivacaftor on CFTR14
Retracing changes in cystic fibrosis understanding and management over the past twenty years14
160 LUNAR-CFTR mRNA improves mucociliary clearance in cystic fibrosis ferrets14
WS19.01 Non-adherence in the twilight zone: the complexity of complex medications14
102 Clinical Pseudomonas aeruginosa isolates from cystic fibrosis sinusitis prevent flagellin-mediated immune recognition14
626: VX-770 does not efficiently activate human CFTR in digitonin14
552 Using the TriNetX database to describe the prevalence of VTE and gastrointestinal disease in children with cystic fibrosis13
37 Antibiotics to treat common cystic fibrosis airway pathogens influence susceptibility to Mycobacterium abscessus lung infection13
643: A novel splice modulator compound corrects splicing defect caused by c.2988G >A variant in CFTR13
649 Decreasing waiting room times in a cystic fibrosis clinic: a quality improvement project13
412 Increasing the number of people with cystic fibrosis seen in outpatient clinic quarterly13
P249 Awareness of the potential benefits of occupational therapy in a cystic fibrosis multidisciplinary team13
542 Improving nutrition outcomes through implementation of a standardized nutrition treatment algorithm in infants with cystic fibrosis younger than 213
569 Symptom changes throughout the menstrual cycle in women with cystic fibrosis13
49 Bacterial siderophores drive cefiderocol resistance and crossprotection13
476 “Thin and watery”: online discussions of sexual and reproductive health by men with cystic fibrosis13
434: Interspecies signaling during cystic fibrosis airway infection: How cAMP and c-di-GMP direct Pseudomonas aeruginosa chemotaxis toward Staphylococcus aureus13
461: Unraveling the role of IL-17 receptor C during development of airway chronic infections by Pseudomonas aeruginosa13
544: Safety and tolerability of single and repeat doses of MRT5005, an inhaled CFTR mRNA replacement therapy, in adult CF patients13
523: Prevalence of Staphylococcus aureus in cystic fibrosis with reduced susceptibility to beta-lactam antibiotics at high inoculum13
1 High Ca++ does not hinder cyclic diguanosine monophosphate–mediated control of the Pseudomonas aeruginosa biofilm life cycle13
521: Dual targeting of host and fungal sphingosine-1-phosphate lyase as antifungal strategy in cystic fibrosis13
482 Changing the conversation: exploring the influence of participation in a withdrawal study on clinical communication13
414 National patterns of CF RISE uptake and engagement: a multidimensional approach to increase transition program utilization13
363: Losartan increases the efficacy of CFTR modulators to reverse inflammation-related mucociliary dysfunction13
385: Generation of FOXi1-KO ferrets using CRISPR/Cas9 gene editing to inform pulmonary ionocyte biology12
401 Black and Hispanic people with cystic fibrosis (PwCF) and PwCF with high lung function are less likely to be prescribed elexacaftortezacaftor-ivacaftor despite having an eligible genotype12
ePS3.07 Exploring the therapeutic potential of iminosugars as antibacterial and antibiofilm agents in the treatment of cystic fibrosis lung disease infections12
P030 Effect of CFTR modulators on lung function, body mass index, and Pseudomonas aeruginosa status in adolescents with cystic fibrosis - one-year follow-up12
245 Generation of airway basal stem cells from induced pluripotent stem cell–derived airway progenitors: elucidation of signaling pathways responsible for basal cell maturation and proliferation12
151: Time to prescription of Trikafta for remote and local dwelling patients with cystic fibrosis12
395 Health equities assessment—Southern California Research Consortium12
P001 Cystic fibrosis newborn screening (CF-NBS) start-up in Flanders (Belgium): report of first evaluation after 3 years12
ePS2.04 Is tele-physiotherapy as effective as home-visit-guided physiotherapy among children with cystic fibrosis?12
374: Rheological comparison of solubility and gel permanence between airway mucin solutions and mucus systems12
P046 The effectiveness of CFTR modulators in people with cystic fibrosis and rare mutations – a real-world study12
375: Exposure to healthy or cystic fibrosis sputum alters ion transport across human bronchial epithelial cells12
398 Reducing costs for testing related to positive cystic fibrosis newborn screens12
ePS4.08 COVID-19 vaccine uptake in adult people with cystic fibrosis12
P024 Patient-derived organoids as a model for treatment diagnosis in cystic fibrosis – combinatory treatment with read-through agent, correctors and potentiator on rare mutations12
161: Inter-visit reproducibility of free-breathing lung magnetic resonance imaging in cystic fibrosis12
239 Organoid-guided synergistic treatment of minimal function CFTR mutations with CFTR modulators, roflumilast and simvastatin: A personalized approach12
P071 The characterisation of a patient cohort that had home spirometry devices and opted into sharing their data with the US Cystic Fibrosis Foundation12
60: The real-world effectiveness of U.S. CF newborn screening11
P171 Improved diagnosis and treatment of distal intestinal obstruction syndrome (DIOS) with a simplified treatment routine11
293: Perceptions and understanding of CFTR modulators11
38: Real-world longitudinal trends in clinical outcomes in people with cystic fibrosis using lumacaftor/ivacaftor and tezacaftor/ivacaftor11
328: What COVID taught us—Collaboration in pursuit of expanded paid leave11
WS05.05 Proximity profiling of the CFTR interaction landscape in response to Orkambi11
344 Unraveling the complexity of cystic fibrosis: genetic modifiers and their roles in cystic fibrosis pathogenesis11
327 Data analysis for large-scale theratyping study of 656 CFTR variants11
83: CF Global Care: Continuation of the collaboration between 2 CF centers; University of Michigan, USA, and Marmara University, Istanbul, Turkey, in the COVID-19 pandemic11
53: Distinct early life growth trajectories in CF are associated with lung function at 6 years11
P208 A retrospective observational study of the effects of Kaftrio® on the current cohort of patients at Nottingham University Hospitals NUH trust11
22: Unique challenges of treating women with cystic fibrosis–related diabetes in pregnancy11
WS04.05 What is the scope for colorectal cancer screening in cystic fibrosis? Ten years of experience at a UK cystic fibrosis centre11
339 Diagnostic dilemmas in cystic fibrosis screen–positive infants with F191V and low sweat chloride11
WS20.03 What to hope for when there is no hope11
79: A patient satisfaction survey regarding the use of telemedicine for outpatient CF endocrinology and diabetes care during the COVID-19 pandemic11
349 Intestinal epithelial-specific Cftr knockout induces fecal dysbiosis and bowel inflammation in mice consuming anti-obstructive dietary regimens11
WS10.02 People with cystic fibrosis on elexacaftor/tezacaftor/ivacaftor therapy demonstrate improved physical activity levels and cardiovascular fitness11
P147 In vitro sensitivity of Gram-negative cystic fibrosis isolates to a 4th generation fluoroquinolone11
WS04.02 Clinical impact of pathogenic CFTR mutations in paediatric-onset pancreatitis (preliminary analysis from the APPLE study)11
333 Assessing CFTR modulator response for an individual with H609R/ 2184insA using different in-vitro model systems11
394 Elexacaftor/tezacaftor/ivacaftor interferes with hippocampal neurotransmission in mice10
330 Rescue of CFTR nonsense mutations is enhanced under inflammatory stimuli10
207 Enhancing apical loop currents in airway epithelia carrying minimal function CFTR mutations10
154 Inhibition of the intermediate (KCa3.1) and small (KCa2.3 and KCa2.2) conductance, Ca2+-activated K+ channels by CFTR correctors10
Infection prevention and control in cystic fibrosis: An update of a systematic review of interventions10
Coping and learning to Manage Stress with cystic fibrosis (CALM): A multisite telehealth randomized controlled trial to reduce depression and anxiety symptoms in adults with cystic fibrosis10
P460 Assessing the exercise capacity of adolescents with cystic fibrosis in the post elexacaftor/tezacaftor/ivacaftor era, via cardiopulmonary exercise test10
P462 Applicability of A-STEP performance test in patients diagnosed with cystic fibrosis in Turkish population10
865 Elexacaftor/tezacaftor/ivacaftor concentrations are similar in transplanted and non-transplanted people with CF10
Contents10
693 Machine learning analysis of continuous glucose monitoring after elexacaftor/tezacaftor/ivacaftor initiation in young children predicts dysglycemia better than an oral glucose tolerance test10
4: The effect of elexacaftor/tezacaftor/ivacaftor on glycemia in adults with cystic fibrosis: A prospective continuous glucose monitoring study10
P006 False negative newborn screen and absent clinical features of cystic fibrosis after in utero modulator exposure for an infant with two cystic fibrosis causing mutations10
650 Single-center cohort study evaluating quality of colonoscopy bowel preparation in adults with cystic fibrosis10
4 Within-lung interspecies gene transfer causes rapid evolution of extreme antibiotic resistance in cystic fibrosis10
513 Elexacaftor/tezacaftor/ivacaftor dose reduction leads to resolution of clinical adverse events without a significant effect on sweat chloride or FEV110
Olfactory loss in people with cystic fibrosis: Community perceptions and impact10
Diagnosing constipation in patients with cystic fibrosis applying ESPGHAN criteria10
Implementation of standardized cystic fibrosis care algorithm to improve the center data-quality improvement project international collaboration10
No patient left behind! Therapeutic options for cystic fibrosis patients living with lung transplantation10
P359 The impact of elexacfator/tezacaftor/ivacaftor on the weight trajectories of children and adolescents and predictive factors9
EPS10.10 Elexacaftor/tezacaftor/ivacaftor remains inaccessible for people with cystic fibrosis in low- and middle-income countries: how can this be solved?9
P236 Investigating the impact of elexacaftor/tezacaftor/ivacaftor therapy on longitudinal oropharyngeal microbiome dynamics in children with cystic fibrosis9
P229 Do CFTR modulators interfere with microbiological diagnosis?9
P262 Lack of association between antibiotic regimen spectrum and pulmonary exacerbation treatment responses9
P280 Rapid review of the outcome measures and endpoints used to measure gastrointestinal disease in cystic fibrosis (CARDS-CF study)9
Contents Page9
P052 Real-life experience with a generic formulation of elexacaftor/tezacaftor/ivacaftor in patients with cystic fibrosis and responsive CFTR variants with previous modulators therapy9
P316 Increasing numbers of pregnancies due to modulator therapy in cystic fibrosis9
P306 Analysis risk factors for the decrease bone mineral density in cystic fibrosis9
P125 Development of a holistic feedback package to support quality improvement in cystic fibrosis centres in the UK9
WS08.04 Assessment of functional exercise capacity using telehealth: reliability, validity, and usability in children with cystic fibrosis9
P363 A retrospective review of fat-soluble vitamins A, D and E levels and vitamin supplementation in a cystic fibrosis (CF) maternal health population9
817 Harnessing the power of the electronic medical record to implement the new cystic fibrosis liver disease guidelines8
211 Characterization of airway submucosal gland hypertrophy in cystic fibrosis8
38 ACE-1b, a novel anti-infective conjugated electrolyte, effectively controls nontuberculous mycobacterial infections8
469 Impact of social complexity on long-term health outcomes and survival in young adults with cystic fibrosis8
308 Ligand-free biodegradable poly(beta-amino ester) nanoparticles for targeted systemic delivery of mRNA to the lungs8
233 Altered role of septins in Pseudomonas aeruginosa intracellular infection of cystic fibrosis bronchial epithelial cells8
551 Integration of psychosocial screening tool into routine care of children with CF: Results of a 1-year pilot study and lessons learned8
628 Esophagogastroduodenoscopy findings in adults with cystic fibrosis: implications for screening and management8
75 Improvements in nutritional status, lung function, and respiratory cultures in pediatric cystic fibrosis after starting elexacaftor/tezacaftor/ivacaftor therapy: A real-world, multicenter study8
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